Li Yun-Tian, Luo Wen-Guang, Zhang Hong-Yan
The First Affiliated Hospital of USTC, Division of Life Sciences and Medicine, University of Science and Technology of China, Hefei, Anhui, P.R. China.
Rare Tumors. 2021 May 18;13:20363613211016121. doi: 10.1177/20363613211016121. eCollection 2021.
Epithelioid sarcoma (ES) was first described by Enzinger in 1970. It is a rare variant of soft tissue sarcoma with a 5-year overall survival (OS) rate of 50%. Here, we reported a case of epithelioid sarcoma in the parapharyngeal space of an adult, resulting in a favorable prognosis after chemotherapy and radiation therapy. A 34-year-old female who complained of pharynx pain and discomfort was suspected of having a tumor in the right parapharyngeal space by CT scan. Excision biopsy suggested epithelioid sarcoma. Clinical and radiological studies did not reveal tumor distant metastasis in the patient. After excisional biopsy, the patient underwent chemotherapy and external beam radiation treatment. She has remained alive for 2 years and 7 months without recurrence since her last treatment. In this paper, we also provide a detailed review of the role of radiotherapy in the treatment of epithelioid sarcoma in previously reported cases.
上皮样肉瘤（ES）于1970年由恩津格首次描述。它是软组织肉瘤的一种罕见变体，5年总生存率（OS）为50%。在此，我们报告了一例发生于成人咽旁间隙的上皮样肉瘤病例，经化疗和放疗后预后良好。一名34岁女性因咽部疼痛和不适就诊，CT扫描怀疑其右侧咽旁间隙有肿瘤。切除活检提示为上皮样肉瘤。临床和影像学检查未发现该患者有肿瘤远处转移。切除活检后，患者接受了化疗和外照射治疗。自上次治疗以来，她已存活2年7个月，无复发。在本文中，我们还对放疗在既往报道病例中治疗上皮样肉瘤的作用进行了详细综述。
