Okubo S, Kunieda T, Ando M, Nakajima N, Yutani C
National Cardiovascular Center, Suita City, Osaka, Japan.
Chest. 1988 Sep;94(3):665-6. doi: 10.1378/chest.94.3.665.
Multiple obstructions of the proximal pulmonary arteries were found in a patient with pulmonary hypertension and chronic cor pulmonale without any systemic arterial lesions. An operation to relieve severe stenosis at the right main pulmonary artery provided great clinical improvement. Pathologic examination of the biopsied specimen revealed a nonspecific panarteritis with giant cells consistent with idiopathic isolated pulmonary arteritis.
在一名患有肺动脉高压和慢性肺源性心脏病且无任何体动脉病变的患者中，发现近端肺动脉多处阻塞。对右主肺动脉严重狭窄进行的手术带来了显著的临床改善。活检标本的病理检查显示为非特异性巨细胞性全动脉炎，符合特发性孤立性肺动脉炎。
