Milo S, Fiegel A, Shem-Tov A, Neufeld H N, Goor D A
Department of Thoracic and Cardiovascular Surgery, Sheba Medical Centre, Tel Hashomer, Israel.
Br Heart J. 1988 Aug;60(2):128-33. doi: 10.1136/hrt.60.2.128.
In the 12 years from 1975 to 1987, 55 patients had open pulmonary valve surgery for isolated congenital stenosis of the pulmonary valve. Three types of pulmonary stenosis were seen: (a) dome-shaped pulmonary stenosis (34 patients); (b) dysplastic pulmonary valves with thick cauliflower-like cusps (12 patients), and (c) hour-glass deformity of the pulmonary valve, with "bottle-shaped" sinuses (nine patients). This third type has not been described before. Preoperative identification of the valve structure is important because the choice of treatment (balloon dilatation for some dome-shaped valves and excision for dysplastic and hour-glass valves) depends on the type of stenosis.
在1975年至1987年的12年间，55例患者因单纯先天性肺动脉瓣狭窄接受了肺动脉瓣开放手术。观察到三种类型的肺动脉狭窄：(a) 圆顶状肺动脉狭窄（34例患者）；(b) 发育异常的肺动脉瓣，瓣叶增厚呈菜花状（12例患者）；(c) 肺动脉瓣沙漏样畸形，伴有“瓶状”窦（9例患者）。第三种类型此前未曾有过描述。术前明确瓣膜结构很重要，因为治疗方式的选择（一些圆顶状瓣膜采用球囊扩张术，发育异常和沙漏样瓣膜采用切除术）取决于狭窄的类型。
