Department of Gynecologic Oncology, Beaumont Health, Royal Oak, Michigan, USA
Department of Gynecologic Oncology, Beaumont Health, Royal Oak, Michigan, USA.
BMJ Case Rep. 2021 Jun 30;14(6):e241550. doi: 10.1136/bcr-2021-241550.
Aggressive angiomyxoma (AA) is a rare mesenchymal tumour that is characterised by increased incidence in women compared with men, local invasion to the surrounding tissue and high recurrence rate. A premenopausal woman presented to clinic with pelvic pressure, intermittent tingling in the thigh and pressure emptying the bladder. CT scan, vaginal and gluteal biopsies, and MRI scan were performed to conclude a final diagnosis of AA. The patient underwent complete resection of the mass. The mass tested positive for oestrogen receptor and progesterone receptor. The patient received leuprolide postoperatively to prevent recurrence. AA should be considered as a differential diagnosis for a pelvic and perineal mass. Patients should be warned of high recurrence rate, necessity of surgical removal and long-term hormonal treatment.
侵袭性血管黏液瘤（AA）是一种罕见的间叶组织肿瘤，其特征是女性发病率高于男性，易向周围组织侵袭，且复发率高。一名绝经前女性因盆腔压迫感、大腿间歇性刺痛和排尿困难就诊。进行 CT 扫描、阴道和臀活检及 MRI 扫描，以明确 AA 的最终诊断。患者接受了肿块的完全切除术。该肿块雌激素受体和孕激素受体检测均为阳性。术后患者接受了亮丙瑞林治疗以预防复发。AA 应作为盆腔和会阴肿块的鉴别诊断。应告知患者复发率高、手术切除和长期激素治疗的必要性。
