Menon Sabarinath, Saxena Mch Shivang, M S Rajalakshmi
Division of Pediatric Cardiac Surgery, Department of Cardiovascular and Thoracic surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.
Department of Cardiovascular and Thoracic surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.
J Card Surg. 2021 Feb;36(2):720-722. doi: 10.1111/jocs.15220. Epub 2020 Dec 7.
Hemolytic anemia often challenges congenital heart surgery. Hereditary spherocytosis is a rare familial hemolytic anemia. When associated with congenital heart disease, the safe performance of cardiopulmonary bypass becomes a priority. The increased risk of hemolysis during cardiopulmonary bypass could potentially lead to significant secondary organ damage. Till now, only very few reports of successful repair of a congenital heart defect in patients with hereditary spherocytosis have been reported. We report the only case of successful repair of a congenital heart defect in an infant with hereditary spherocytosis.
溶血性贫血常常给先天性心脏手术带来挑战。遗传性球形红细胞增多症是一种罕见的家族性溶血性贫血。当与先天性心脏病相关时，安全进行体外循环成为首要任务。体外循环期间溶血风险增加可能会导致严重的继发性器官损伤。到目前为止，仅有极少数关于遗传性球形红细胞增多症患者成功修复先天性心脏缺陷的报道。我们报告了一例患有遗传性球形红细胞增多症的婴儿成功修复先天性心脏缺陷的唯一病例。
