Faculty of Medicine, Ramathibodi Hospital, Mahidol University, Bangkok, Thailand.
bluebird bio, Inc., Cambridge, MA.
Blood Adv. 2021 Jul 13;5(13):2701-2706. doi: 10.1182/bloodadvances.2020003680.
Betibeglogene autotemcel (beti-cel) gene therapy (GT) for patients with transfusion-dependent β-thalassemia uses autologous CD34+ cells transduced with BB305 lentiviral vector (LVV), which encodes a modified β-globin gene. BB305 LVV also contains select HIV sequences for viral packaging, reverse transcription, and integration. This case report describes a patient successfully treated with beti-cel in a phase 1/2 study (HGB-204; #NCT01745120) and subsequently diagnosed with wild-type (WT) HIV infection. From 3.5 to 21 months postinfusion, the patient stopped chronic red blood cell transfusions; total hemoglobin (Hb) and GT-derived HbAT87Q levels were 6.6 to 9.5 and 2.8 to 3.8 g/dL, respectively. At 21 months postinfusion, the patient resumed transfusions for anemia that coincided with an HIV-1 infection diagnosis. Quantitative polymerase chain reaction assays detected no replication-competent lentivirus. Next-generation sequencing confirmed WT HIV sequences. Six months after starting antiretroviral therapy, total Hb and HbAT87Q levels recovered to 8.6 and 3.6 g/dL, respectively, and 3.5 years postinfusion, 13.4 months had elapsed since the patient's last transfusion. To our knowledge, this is the first report of WT HIV infection in an LVV-based GT recipient and demonstrates persistent long-term hematopoiesis after treatment with beti-cel and the ability to differentiate between WT HIV and BB305-derived sequences.
贝替贝洛根自体造血干祖细胞(贝替细胞)基因治疗(GT)用于依赖输血的β-地中海贫血患者,使用携带 BB305 慢病毒载体(LVV)的自体 CD34+细胞转导,该载体编码修饰的β-珠蛋白基因。BB305 LVV 还包含用于病毒包装、逆转录和整合的选择 HIV 序列。本病例报告描述了一名患者在 1/2 期研究(HGB-204;#NCT01745120)中成功接受贝替细胞治疗,随后被诊断为野生型(WT)HIV 感染。在输注后 3.5 至 21 个月,患者停止了慢性红细胞输血;总血红蛋白(Hb)和 GT 衍生的 HbAT87Q 水平分别为 6.6 至 9.5 和 2.8 至 3.8 g/dL。在输注后 21 个月,患者因贫血恢复输血,同时诊断出 HIV-1 感染。定量聚合酶链反应检测未发现复制能力的慢病毒。下一代测序证实了 WT HIV 序列。开始抗逆转录病毒治疗后 6 个月,总 Hb 和 HbAT87Q 水平分别恢复至 8.6 和 3.6 g/dL,输注后 3.5 年,患者最后一次输血后 13.4 个月。据我们所知,这是首例 LVV 基 GT 受者中 WT HIV 感染的报告,证明了贝替细胞治疗后的持续长期造血能力,以及区分 WT HIV 和 BB305 衍生序列的能力。