Department of Radiology, Kalafong Hospital, University of Pretoria, South Africa.
S Afr J Surg. 2021 Jun;59(2):66a-66f.
Dermatofibrosarcoma protuberans (DFSP) is a rare, slow-growing, spindle cell neoplasm with low to intermediate grade malignant potential, commonly found in young and middle-aged adults, more in males than females. DFSP mostly originates in the dermis; rarely, it may be located in the deeper tissues without dermal involvement. Typically, DFSP appears as a multinodular mass, which then spreads into the subcutaneous tissues and muscle; it rarely dedifferentiates to high-grade fibrosarcoma, and more rarely, it may metastasise. We describe magnetic resonance imaging (MRI) features in three female patients with histologically proven DFSP and review the literature.
隆突性皮肤纤维肉瘤(DFSP)是一种罕见的、生长缓慢的梭形细胞肿瘤,具有低度至中度恶性潜能,常见于中青年人群,男性多于女性。DFSP 主要起源于真皮;极少数情况下,它可能位于真皮无受累的深部组织中。典型的 DFSP 表现为多结节肿块,然后扩散至皮下组织和肌肉;它很少向高级纤维肉瘤分化,更罕见的情况下,它可能转移。我们描述了 3 例经组织学证实的 DFSP 女性患者的磁共振成像(MRI)特征,并复习了文献。