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晕厥与心脏压塞:原发性心脏淋巴瘤的多模态成像

Syncope and Cardiac Tamponade: Multimodality Imaging of Primary Cardiac Lymphoma.

作者信息

Serra Virginia, De Luca Francesco, Savino Ketty, Pinto Maurizio Del, Castellani Claudia, Fiaschini Paola, Tomasello Laura, Cavallini Claudio

机构信息

Cardiology and Cardiovascular Physiopathology, University of Perugia, Perugia, Italy.

Department of Cardiology, Perugia Hospital, Perugia, Italy.

出版信息

J Cardiovasc Echogr. 2021 Jan-Mar;31(1):42-44. doi: 10.4103/jcecho.jcecho_109_20. Epub 2021 May 21.

DOI:10.4103/jcecho.jcecho_109_20
PMID:34221886
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8230158/
Abstract

Primary cardiac lymphoma (PCL) is among the rarest heart neoplasms. Its estimated incidence is about 1%-2% among primary cardiac tumor and 0.5% of extranodal lymphoma. It usually causes heart failure, pericardial effusion, tamponade, and arrhythmias. Prognosis is poor; treatment is combined medical and surgical. We described the case of a 62-year-old male with PLC that presented with syncope and cardiac tamponade, submitted to R-CHOP therapy because of failure of surgery. Clinical state is stable 3 months after diagnosis and first chemotherapy cycle.

摘要

原发性心脏淋巴瘤(PCL)是最罕见的心脏肿瘤之一。其在原发性心脏肿瘤中的估计发病率约为1%-2%,在结外淋巴瘤中占0.5%。它通常会导致心力衰竭、心包积液、心脏压塞和心律失常。预后较差;治疗采用药物和手术相结合的方式。我们描述了一例62岁患有原发性心脏淋巴瘤的男性患者,该患者表现为晕厥和心脏压塞,因手术失败而接受R-CHOP治疗。诊断和首个化疗周期3个月后临床状态稳定。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/48bc5d8ce832/JCE-31-42-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/e6f47c6df322/JCE-31-42-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/91284ae3ae63/JCE-31-42-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/130b850ea782/JCE-31-42-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/745b31c24b80/JCE-31-42-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/48bc5d8ce832/JCE-31-42-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/e6f47c6df322/JCE-31-42-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/91284ae3ae63/JCE-31-42-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/130b850ea782/JCE-31-42-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/745b31c24b80/JCE-31-42-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6eae/8230158/48bc5d8ce832/JCE-31-42-g005.jpg

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本文引用的文献

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Cardiac Lymphoma.心脏淋巴瘤
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Tex Heart Inst J. 2014 Dec 1;41(6):657-9. doi: 10.14503/THIJ-13-3595. eCollection 2014 Dec.
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A rare case of primary cardiac B cell lymphoma.原发性心脏B细胞淋巴瘤1例罕见病例。
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