Tropet Y, Menez D, Runge M, Vichard P
Service d'Orthopédie-Traumatologie, CHU de Besançon, Hôpital Jean Minjoz.
Ann Chir Main. 1987;6(2):140-3. doi: 10.1016/s0753-9053(87)80028-5.
The authors describe a case of melorheostosis localised in the hand. Melorheostosis is an unusual affection. The first signs appear in some cases at birth, but the disease is often diagnosed during the fourth decade. Clinical symptoms are pain, ankylosis, the deformation provoked by the lesion of soft tissues and especially limitation of motion. Radiographs permit the diagnosis: opacities parallel to the diaphysis with a "monomelic" topography. The natural history of the condition is characterized by the possibility of extension of the disease. Operative treatment is rarely indicated.
作者描述了一例局限于手部的骨密质增生症。骨密质增生症是一种罕见的病症。在某些情况下,最初症状在出生时就会出现,但该病通常在四十岁左右被诊断出来。临床症状包括疼痛、关节强直、软组织损伤引起的畸形,尤其是活动受限。X线片有助于诊断:与骨干平行的不透光区呈“单肢”分布。该病的自然病程特点是有病情扩展的可能。很少需要进行手术治疗。