不同病因的成人外周肺动脉狭窄患者的治疗困境
The treatment dilemma in adult patients with peripheral pulmonary artery stenosis of diverse etiologies.
作者信息
Hosseini Zahra, Firouzi Ata, Mohebbi Bahram, Khalilipur Ehsan, Baay Mohammadreza, Kalantari Kiara Rezaei, Harirforoosh Iman, Khajali Zahra
机构信息
Cardiovascular Intervention Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Vali-Asr Ave, Tehran, 1996911101, Iran.
出版信息
Egypt Heart J. 2021 Jul 15;73(1):65. doi: 10.1186/s43044-021-00190-5.
BACKGROUND
Peripheral pulmonary artery stenosis (PPAS) is a rare and underdiagnosed phenomenon that is reported infrequently in adult patients. Most patients with PPAS have concomitant congenital heart diseases, a history of palliative surgical therapies during childhood, or syndromic characteristics. Acquired cases are rare, and they are underestimated in adulthood and managed inappropriately.
CASE PRESENTATION
This case series describes 3 adult patients with PPAS of diverse etiologies and discusses their underlying causes, diagnostic modalities, and treatment strategies.
CONCLUSIONS
In patients with PPAS, sufficient heed should be paid to endovascular interventions such as balloon dilation and primary or bailout stenting, not least vis-à-vis the type and size of balloons or stents as well as complications and preventive strategies.
背景
外周肺动脉狭窄（PPAS）是一种罕见且诊断不足的现象，在成年患者中报道较少。大多数PPAS患者伴有先天性心脏病、儿童期姑息性手术治疗史或综合征特征。后天性病例罕见，在成年期被低估且治疗不当。
病例报告
本病例系列描述了3例病因各异的成年PPAS患者，并讨论了其潜在病因、诊断方法和治疗策略。
结论
对于PPAS患者，应充分重视血管内介入治疗，如球囊扩张和初次或补救性支架置入，尤其要关注球囊或支架的类型和尺寸以及并发症和预防策略。
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