Bakalli Aurora, Jashari Imri, Krasniqi Xhevdet, Spahiu Lidvana
Clinic of Invasive Cardiology and Cardiosurgery, University Clinical Center of Kosova and Medical Faculty, University of Prishtina, Pristina, Kosovo.
Clinic of Cardiology, University Clinical Center of Kosova, Pristina, Kosovo.
Clin Med Insights Case Rep. 2021 Jul 2;14:11795476211017733. doi: 10.1177/11795476211017733. eCollection 2021.
Dextrocardia is a rare congenital anomaly, whereas its association with sick sinus syndrome in young adults without accompanying heart abnormalities is exceptional. We report a case of a 38 year old female patient who was admitted to our hospital due to syncope as a consequence of sinus pauses up to 4.9 seconds. She was also diagnosed with situs inversus totalis, with mirror image dextrocardia. Pacemaker implantation was indicated. Under local anesthesia, from the left subclavian vein, the guide wire was passed through superior vena cava to the right atrium and ventricle without any obstacles. In conclusion, situs inversus totalis with mirror image dextrocardia may present in combination with sick sinus syndrome as early as the fourth decade of life. Implantation of pacemaker leads from the left subclavian vein appears accessible and safe in patients with dextrocardia with situs inversus (mirror image).
右位心是一种罕见的先天性异常,而在无心脏伴随异常的年轻成年人中,其与病态窦房结综合征相关则更为罕见。我们报告一例38岁女性患者,因长达4.9秒的窦性停搏导致晕厥而入住我院。她还被诊断为完全性内脏转位伴镜像右位心。需要植入起搏器。在局部麻醉下,导丝从左锁骨下静脉穿过上腔静脉,顺利进入右心房和右心室。总之,完全性内脏转位伴镜像右位心可能早在生命的第四个十年就与病态窦房结综合征同时出现。对于右位心伴内脏转位(镜像)的患者,从左锁骨下静脉植入起搏器导线似乎可行且安全。