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先天性共轭水平眼球运动缺失。

Congenital absence of conjugate horizontal eye movements.

作者信息

Kruis J A, Houtman W A, Van Weerden T W

机构信息

Department of Ophthalmology, University Hospital Groningen, The Netherlands.

出版信息

Doc Ophthalmol. 1987 Sep-Oct;67(1-2):13-8. doi: 10.1007/BF00142692.

Abstract

Loss of conjugate horizontal eye movements is usually due to a lesion in the pons (tumour, vascular, M.S.). However, the condition may also be congenital, either isolated or as part of Moebius's syndrome. Three patients with congenital absence of all conjugate horizontal eye movements are described. In two of them a conjugate pendular nystagmus was observed. Two of the three patients suffered from progressive scoliosis. Congenital absence of all conjugate horizontal eye movements, associated with progressive scoliosis, probably forms a separate clinical entity.

摘要

共轭水平眼球运动丧失通常是由于脑桥病变(肿瘤、血管病变、多发性硬化症)。然而,这种情况也可能是先天性的,可为孤立性或作为莫比乌斯综合征的一部分。本文描述了三名先天性完全缺乏共轭水平眼球运动的患者。其中两名患者观察到共轭摆动性眼球震颤。三名患者中有两名患有进行性脊柱侧弯。先天性完全缺乏共轭水平眼球运动并伴有进行性脊柱侧弯,可能构成一种独立的临床病症。

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