Instituto Clínic de Oftalmología (ICOF), Hospital Clínic de Barcelona, Barcelona, Spain; Institut d'Investigacions Biomèdiques August Pi I Sunyer (IDIBAPS), Barcelona, Spain.
Instituto Clínic de Oftalmología (ICOF), Hospital Clínic de Barcelona, Barcelona, Spain.
Arch Soc Esp Oftalmol (Engl Ed). 2021 Aug;96(8):449-452. doi: 10.1016/j.oftale.2020.07.009. Epub 2020 Nov 14.
Two cases are reported of acute idiopathic blind spot enlargement syndrome (AIBSE) that presented with peripapillary white spots in the fundus. AIBSE belongs to the acute zonal occult outer retinopathy (AZOOR) complex. Conditions of this AZOOR complex may overlap. Typically, in AIBSE, a peripapillary hyperautofluorescence is seen in the autofluorescence. En-face OCT angiography at the ellipsoid level showed hyper-reflective spots around the optic disk in both cases. One case showed a reversible enlargement of the blind spot in visual field. AZOOR complex is an inflammatory disorder that affects the outer retina, and can now be confirmed with structural optical coherence tomography. In the cases presented, there was a reversible severe loss of the outer retina.
报告了两例急性特发性盲点扩大综合征（AIBSE）病例，眼底可见视盘周围有白色斑点。AIBSE 属于急性区域性隐匿性外层视网膜病变（AZOOR）综合征。该 AZOOR 综合征的情况可能会重叠。通常，在 AIBSE 中，自发荧光中可见视盘周围高自发荧光。在这两种情况下，在椭圆体水平的共焦 OCT 血管造影上均显示在视盘周围有高反射斑点。一例患者的盲点在视野中出现可逆性扩大。AZOOR 综合征是一种影响外视网膜的炎症性疾病，现在可以通过结构光相干断层扫描来确诊。在报告的病例中，外视网膜出现了可逆性严重丧失。
