Barbosa Gabriel Castilho Sandoval, Susanna Bianca Nicolela, Okuno Regis Kassai, Junior Remo Susanna
Department of Ophthalmology, Suel Abujamra Institute, São Paulo, SP, Brazil.
Department of Ophthalmology, ABC Ophthalmology Foundation, Santo André, SP, Brazil.
J Curr Ophthalmol. 2021 Jul 5;33(2):209-211. doi: 10.4103/joco.joco_176_20. eCollection 2021 Apr-Jun.
To report a case of Sturge-Weber syndrome (SWS) complicated with uncontrolled glaucoma and serous retinal detachment (SRD) in the left eye that evolved with complete resolution after trabeculectomy.
We report the case of a 10-year-old boy with SWS complicated with uncontrolled glaucoma and SRD in the left eye. In primary evaluation, he presented with a left-sided nevus flammeus affecting upper eyelid and best corrected visual acuity of 20/50 on the affected eye. Fundus examination revealed glaucomatous optic nerve neuropathy and diffuse choroidal hemangioma with overlying SRD, which were confirmed with spectral domain optical coherence tomography. Right eye was unremarkable.
The patient underwent trabeculectomy with mitomycin-C on the affected eye. Two weeks later, he presented with normalization of the intraocular pressure and substantial resolution of subretinal fluid (SRF), which improved to complete resolution of the SRD at 2 months of follow-up. In addition, there was an improvement of visual acuity from 20/50 to 20/40.
This is the first report to describe a case of SWS associated with SRD and resolution of SRF after trabeculectomy.
报告一例患有斯特奇-韦伯综合征(SWS)且左眼合并难治性青光眼和浆液性视网膜脱离(SRD)的病例,该病例在小梁切除术后视网膜脱离完全消退。
我们报告了一名10岁患有SWS且左眼合并难治性青光眼和SRD的男孩病例。初次评估时,他左侧上睑有火焰状痣,患眼最佳矫正视力为20/50。眼底检查发现青光眼性视神经病变和弥漫性脉络膜血管瘤伴上方SRD,这些通过光谱域光学相干断层扫描得到证实。右眼未见异常。
该患者患眼接受了丝裂霉素C小梁切除术。两周后,他的眼压恢复正常,视网膜下液(SRF)大幅消退,在随访2个月时SRD完全消退。此外,视力从20/50提高到了20/40。
这是首例描述SWS合并SRD且小梁切除术后SRF消退的病例报告。