Risavi Brian L, Puller Justin, Juhasz Kristin
Lake Erie College of Osteopathic Medicine Erie Pennsylvania USA.
UPMC Hamot Erie Pennsylvania USA.
Clin Case Rep. 2021 Aug 30;9(9):e04750. doi: 10.1002/ccr3.4750. eCollection 2021 Sep.
Dermatomyositis is a rare disease affecting primarily skin and muscles and is associated with malignancies, especially in at-risk patients. Clinical presentations vary widely but proximal muscle weakness and typical skin findings should prompt consideration of the diagnosis. Immunosuppressive therapy is required, as is continued screening for malignant disease during follow-up.
皮肌炎是一种主要影响皮肤和肌肉的罕见疾病,与恶性肿瘤相关,尤其是在高危患者中。临床表现差异很大,但近端肌无力和典型的皮肤表现应促使考虑诊断。需要进行免疫抑制治疗,随访期间也需要持续筛查恶性疾病。