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单心室先天性心脏病中的冠状静脉窦口梗阻:两名结局不同的患者。

Coronary Sinus Ostial Obstruction in Single-Ventricle Congenital Heart Disease: Two Patients With Different Outcomes.

作者信息

Dalby Stephen T, Mitchell William M, Greiten Lawrence E, Reemtsen Brian, Eisenring Christian, Zakaria Dala

机构信息

Arkansas Children's Hospital, Little Rock, Arkansas, USA.

Section of Pediatric Cardiology, Department of Pediatrics, University of Arkansas for Medical Sciences, Little Rock, Arkansas, USA.

出版信息

JACC Case Rep. 2021 Sep 15;3(12):1459-1462. doi: 10.1016/j.jaccas.2021.07.011.

Abstract

Coronary sinus ostial obstruction is an exceedingly rare anomaly that is particularly important to diagnose in patients with single-ventricle heart disease before surgical palliation. We present 2 cases, an infant and an adult, diagnosed with coronary sinus ostial obstruction, with different clinical outcomes due to timing of diagnosis. ().

摘要

冠状静脉窦口梗阻是一种极其罕见的异常情况,对于单心室心脏病患者在手术姑息治疗前进行诊断尤为重要。我们报告2例病例,1例婴儿和1例成人,均被诊断为冠状静脉窦口梗阻,由于诊断时机不同,临床结局各异。()

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5e0/8446230/fe326f474be0/fx1.jpg

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