Division of Pediatric Rheumatology, Department of Pediatrics, Duke University, 2301 Erwin Road, DUMC Box 3212, Durham, NC 27710, USA.
Division of Pediatric Rheumatology, Department of Pediatrics, The University of North Carolina Chapel Hill, 030 MacNider Hall, CB #7231, Chapel Hill, NC 27599, USA; Division of Allergy/Immunology, Department of Pediatrics, The University of North Carolina Chapel Hill, Chapel Hill, NC.
Rheum Dis Clin North Am. 2021 Nov;47(4):781-796. doi: 10.1016/j.rdc.2021.07.007. Epub 2021 Aug 27.
This article provides an overview of the clinical presentation and diagnosis of select pediatric primary systemic vasculitides. Important advances in understanding the pathogenesis of these rare diseases also are discussed and efforts to harmonize treatment through consensus-based guidelines and multicenter and international collaborations highlighted.
本文概述了几种儿科原发性系统性血管炎的临床表现和诊断。还讨论了在理解这些罕见疾病发病机制方面的重要进展,并强调了通过基于共识的指南以及多中心和国际合作来协调治疗的努力。