Department of Pathology, Aleppo University Hospital, Aleppo, Syria.
Division of Neurology, Department of Internal Medicine, Aleppo University Hospital, Aleppo, Syria.
BMC Gastroenterol. 2021 Oct 12;21(1):374. doi: 10.1186/s12876-021-01947-7.
Benign Multicystic Peritoneal Mesothelioma (BMPM) is one of the rarest diseases in medicine with only more than 200 cases worldwide. This paper aims to report a case of Benign Multicystic Peritoneal Mesothelioma that strangely arose from the liver and was long treated as Hydatid cyst. The case also had many risk factors including asbestos exposure that had not yet been linked with Benign Multicystic Peritoneal Mesothelioma.
We report a case of a 62 years old male with a history of a perforated peptic ulcer and a cystic mass in the liver that was misdiagnosed as hydatid cyst 7 years ago. He presented with generalized abdominal pain and bloating. Image studies showed many cystic formations filled with clear fluid. An en bloc surgery was performed and a pathologic study showed a multiloculated mass lined by flat or cuboidal epithelium leading to the diagnosis of BMPM. A follow up was scheduled after 3 months revealed total recurrence.
BMPM resembles many other cystic lesions in the abdomen and should be taken into consideration when dealing with nontypical cystic formations. Its diagnostic and treatment methods are still hazy making this disease difficult to approach.
良性多房性腹膜间皮瘤(BMPM)是医学上罕见的疾病之一,全球仅有超过 200 例病例。本文旨在报告一例罕见的源自肝脏的良性多房性腹膜间皮瘤病例,该病例曾长期被误诊为包虫囊肿。该病例还存在许多风险因素,包括尚未与良性多房性腹膜间皮瘤相关的石棉暴露。
我们报告了一例 62 岁男性病例,该患者曾患有穿透性消化性溃疡病史,7 年前肝脏出现囊性肿块,被误诊为包虫囊肿。他表现为全腹疼痛和腹胀。影像学研究显示多个充满清亮液体的囊性结构。进行了肿块整块切除术,病理研究显示多房性肿块由扁平或立方上皮衬里,最终诊断为 BMPM。术后 3 个月进行了随访,发现完全复发。
BMPM 与腹部许多其他囊性病变相似,在处理非典型囊性病变时应考虑到这种疾病。其诊断和治疗方法仍不明确,使得这种疾病难以治疗。