Khurram Muhammad S, Shaikh Hamadullah, Khan Uqba, Edens Jacob, Ibrar Warda, Hamza Ameer, Zaka Awais, Bano Roohi, Hadid Tarik
St. John Hospital and Medical Center, Detroit, MI 48236, USA.
Champion Orthopedics, Hamilton, NJ, USA.
Case Rep Pathol. 2017;2017:9752908. doi: 10.1155/2017/9752908. Epub 2017 May 18.
Benign Multicystic Peritoneal Mesothelioma (BMPM) is a rare condition that arises from the abdominal peritoneum. Fewer than 200 cases have been reported worldwide. BMPM usually affects premenopausal women and is extremely rare in men. Many factors are suspected to contribute to its development, such as previous surgery, endometriosis, and familial Mediterranean fever. The main management is surgical resection; however, it is estimated that the recurrence rate is up to 50%. Malignant transformation is rare. We report a case series of three male patients who were diagnosed with BMPM and were treated with cytoreductive surgery and hyperthermic intraperitoneal chemotherapy (HIPEC).
良性多囊性腹膜间皮瘤(BMPM)是一种起源于腹膜的罕见病症。全球报告的病例少于200例。BMPM通常影响绝经前女性,在男性中极为罕见。许多因素被怀疑与它的发生有关,如既往手术、子宫内膜异位症和家族性地中海热。主要治疗方法是手术切除;然而,据估计复发率高达50%。恶性转化很少见。我们报告了一组三例男性患者的病例系列,他们被诊断为BMPM,并接受了细胞减灭术和腹腔内热灌注化疗(HIPEC)。