• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

克兰费尔特综合征合并大面积肺栓塞:一例罕见病例报告

Massive Pulmonary Emboli in Klinefelter Syndrome: A Rare Case Report.

作者信息

Javaherforooshzadeh Fatemeh, Torfi Yusef

机构信息

Ahvaz Anesthesiology and Pain Research Center, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran.

Atherosclerosis Research Center, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran.

出版信息

Anesth Pain Med. 2021 Aug 28;11(4):e117808. doi: 10.5812/aapm.117808. eCollection 2021 Aug.

DOI:10.5812/aapm.117808
PMID:34692444
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8520670/
Abstract

INTRODUCTION

Klinefelter syndrome (KS) is a genetic disorder that affects men. An augmented incidence of the thromboembolic event described in patients with KS.

CASE PRESENTATION

A 34-year-old male identified with a definitive diagnosis of KS was hospitalized to our cardiac surgery center through the emergency with chief complaints of acute chest pain and dyspnea. Saddle pulmonary thromboembolism was established from chest Computed Tomography Angiography (CTA). The patient's symptoms resolved after embolectomy via surgery.

CONCLUSIONS

There is a tendency for hypercoagulability in KS. This tendency is because of hormonal discrepancy and hereditary thrombophilic factors. So, patients with KS and past medical history of venous thromboembolism necessitate constant oral anticoagulation therapy.

摘要

引言

克兰费尔特综合征(KS)是一种影响男性的遗传性疾病。KS患者发生血栓栓塞事件的发生率有所增加。

病例报告

一名34岁男性被确诊为KS,因急性胸痛和呼吸困难为主诉通过急诊入住我们的心脏外科中心。胸部计算机断层扫描血管造影(CTA)确诊为马鞍形肺血栓栓塞。患者经手术取栓后症状缓解。

结论

KS患者有高凝倾向。这种倾向是由于激素差异和遗传性血栓形成倾向因素。因此,有KS且有静脉血栓栓塞病史的患者需要持续口服抗凝治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75f1/8520670/caa204bb674e/aapm-11-4-117808-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75f1/8520670/caa204bb674e/aapm-11-4-117808-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/75f1/8520670/caa204bb674e/aapm-11-4-117808-g001.jpg

相似文献

1
Massive Pulmonary Emboli in Klinefelter Syndrome: A Rare Case Report.克兰费尔特综合征合并大面积肺栓塞:一例罕见病例报告
Anesth Pain Med. 2021 Aug 28;11(4):e117808. doi: 10.5812/aapm.117808. eCollection 2021 Aug.
2
A case of severe pulmonary thromboembolism in a young male with klinefelter syndrome.一例克林费尔特综合征年轻男性的严重肺血栓栓塞症。
Korean Circ J. 2012 Aug;42(8):562-4. doi: 10.4070/kcj.2012.42.8.562. Epub 2012 Aug 31.
3
Acute pulmonary embolism as an initial presentation of Klinefelter syndrome.急性肺栓塞作为克兰费尔特综合征的首发表现
J Saudi Heart Assoc. 2020 Apr 17;32(1):114-117. doi: 10.37616/2212-5043.1020. eCollection 2020.
4
Respiratory distress in a patient with Klinefelter syndrome: a suspicion of COVID-19 hiding severe pulmonary embolism.克兰费尔特综合征患者的呼吸窘迫:疑似新型冠状病毒肺炎掩盖了严重肺栓塞
Pan Afr Med J. 2020 Sep 18;37(Suppl 1):13. doi: 10.11604/pamj.supp.2020.37.13.25894. eCollection 2020.
5
Venous thromboembolism and COVID-19: a case report and review of the literature.静脉血栓栓塞症与2019冠状病毒病:一例病例报告及文献综述
J Med Case Rep. 2020 Oct 15;14(1):188. doi: 10.1186/s13256-020-02516-4.
6
Case report: Re-emerging significance of surgical embolectomy in pulmonary embolism.病例报告:外科取栓术在肺栓塞中的重新显现的重要性。
Ann Med Surg (Lond). 2018 Dec 3;39:26-28. doi: 10.1016/j.amsu.2018.11.010. eCollection 2019 Mar.
7
Successful surgical embolectomy in acute massive bilateral pulmonary embolism.急性大面积双侧肺栓塞的成功手术取栓术
J Pak Med Assoc. 2011 May;61(5):498-500.
8
Genetic risk factors for venous thromboembolism among infertile men with Klinefelter syndrome.克兰费尔特综合征不育男性静脉血栓栓塞的遗传风险因素。
J Clin Transl Endocrinol. 2020 May 19;20:100228. doi: 10.1016/j.jcte.2020.100228. eCollection 2020 Jun.
9
[Intracranial hemorrhage due to pulmonary thromboembolism in heparin therapy and therapeutic management of patients hospitalized with massive pulmonary embolism after discharge].[肝素治疗中肺血栓栓塞导致的颅内出血及出院后发生大面积肺栓塞住院患者的治疗管理]
Turk Kardiyol Dern Ars. 2013 Apr;41(3):228-32. doi: 10.5543/tkda.2013.75031.
10
Surgical embolectomy for paradoxical cerebral embolism with massive pulmonary embolism.手术取栓治疗伴有大面积肺栓塞的反常性脑栓塞
Gen Thorac Cardiovasc Surg. 2020 Apr;68(4):385-388. doi: 10.1007/s11748-019-01087-6. Epub 2019 Apr 6.

本文引用的文献

1
Pulmonary Embolism and Cardiac Tamponade in Critical Care Patients with COVID-19; Telemedicine's Role in Developing Countries: Case Reports and Literature Review.COVID-19 危重症患者的肺栓塞和心脏压塞;远程医疗在发展中国家的作用:病例报告与文献综述
Anesth Pain Med. 2021 Apr 7;11(2):e113752. doi: 10.5812/aapm.113752. eCollection 2021 Apr.
2
Klinefelter Syndrome in Childhood: Variability in Clinical and Molecular Findings.儿童克兰费尔特综合征:临床与分子学发现的变异性
J Clin Res Pediatr Endocrinol. 2018 Jun 1;10(2):100-107. doi: 10.4274/jcrpe.5121. Epub 2017 Oct 12.
3
Pulmonary embolism and in situ pulmonary artery thrombosis in paediatrics. A systematic review.
儿童肺栓塞和原位肺动脉血栓形成。系统评价。
Thromb Haemost. 2017 Jun 2;117(6):1199-1207. doi: 10.1160/TH16-07-0529. Epub 2017 Mar 23.
4
Recent developments in the diagnosis and treatment of pulmonary embolism.肺栓塞的诊断与治疗新进展。
J Intern Med. 2016 Jan;279(1):16-29. doi: 10.1111/joim.12404. Epub 2015 Aug 19.
5
2014 ESC guidelines on the diagnosis and management of acute pulmonary embolism.2014年欧洲心脏病学会急性肺栓塞诊断和管理指南
Eur Heart J. 2014 Nov 14;35(43):3033-69, 3069a-3069k. doi: 10.1093/eurheartj/ehu283. Epub 2014 Aug 29.
6
Diagnosis and classification of the antiphospholipid syndrome.抗磷脂综合征的诊断和分类。
J Autoimmun. 2014 Feb-Mar;48-49:20-5. doi: 10.1016/j.jaut.2014.01.006. Epub 2014 Jan 24.
7
Inflammatory bowel disease: epidemiology, pathology and risk factors for hypercoagulability.炎症性肠病:流行病学、病理学和高凝状态的危险因素。
World J Gastroenterol. 2014 Jan 7;20(1):53-63. doi: 10.3748/wjg.v20.i1.53.
8
A case of severe pulmonary thromboembolism in a young male with klinefelter syndrome.一例克林费尔特综合征年轻男性的严重肺血栓栓塞症。
Korean Circ J. 2012 Aug;42(8):562-4. doi: 10.4070/kcj.2012.42.8.562. Epub 2012 Aug 31.