Department of Pediatrics and Child Health, Jimma University.
Department of Radiology, Jimma University.
Ethiop J Health Sci. 2021 Jul;31(4):903-906. doi: 10.4314/ejhs.v31i4.26.
A pouch protruding from the free wall of the left ventricle may be either a congenital ventricular diverticulum or congenital ventricular aneurysm. Congenital ventricular aneurism is a ventricular protuberance which is a kinetic or dyskinetic and on histology is predominantly fibrous tissue with no organized myocardium. Common clinical presentations of congenital ventricular aneurism are arrhythmia, rupture and heart failure.
A 13 year old patient presented with shortness of breath, fever, orthopnea of two pillows and paroxysmal nocturnal dyspnea of one week duration. Echocardiography revealed cystic mass seen at the apex of the heart communicating with left ventricle, with communicating defect and flow on color Doppler study. CT scan showed ventricular aneurism at the apex. The patient was managed for heart failure and passed away after few hours' of establishing diagnosis.
Congenital ventricular aneurysm is a rare condition which needs careful diagnosis for subsequent management.
从左心室游离壁突出的囊袋可能是先天性心室憩室或先天性心室动脉瘤。先天性心室动脉瘤是心室的一种隆起,它是一种动力性或无动力性的,组织学上主要是纤维组织,没有有组织的心肌。先天性心室动脉瘤的常见临床表现为心律失常、破裂和心力衰竭。
一名 13 岁患者因呼吸困难、发热、两个枕头的端坐呼吸和一周阵发性夜间呼吸困难而就诊。超声心动图显示心脏尖部可见囊性肿块与左心室相通,彩色多普勒研究显示有相通的缺损和血流。CT 扫描显示心尖部有室壁瘤。患者因心力衰竭接受治疗,在确诊后数小时内死亡。
先天性心室动脉瘤是一种罕见的疾病,需要仔细诊断以进行后续治疗。