Kawahara M, Takeshita T, Akita S
Anesth Prog. 1987 Jan-Feb;34(1):17-9.
Kasabach-Merritt syndrome presents various problems for anesthetic management, which include thrombocytopenia, bleeding tendency, and problems arising from the hemangioma mass itself. A 20-month-old female was scheduled for cryosurgery of a hemangioma on the face. Massive bleeding from the tumor was easily induced even by slight contact. The hematologic examination revealed a low platelet count and anemia. Anesthesia was induced carefully by applying an adult anesthetic mask to avoid the large tumor mass on the face and maintained with halothane and nitrous oxide/oxygen. Additional doses of prednisolone were administered before and during anesthesia to compensate for possible adrenal insufficiency due to steroid therapy which she had been receiving. Neither excessive bleeding nor any other particular complications occurred during anesthesia and surgery, and the postoperative course was also uneventful.
卡萨巴赫-梅里特综合征给麻醉管理带来了各种问题，包括血小板减少、出血倾向以及血管瘤肿块本身引发的问题。一名20个月大的女性计划接受面部血管瘤冷冻手术。即使轻微接触也很容易导致肿瘤大量出血。血液学检查显示血小板计数低和贫血。通过使用成人麻醉面罩小心诱导麻醉，以避开面部的大肿瘤肿块，并使用氟烷和氧化亚氮/氧气维持麻醉。在麻醉前和麻醉期间额外给予泼尼松龙剂量，以补偿她因一直接受的类固醇治疗可能导致的肾上腺功能不全。麻醉和手术期间既没有发生过度出血，也没有出现任何其他特殊并发症，术后过程也很顺利。
