Irungu Anne, Achola Cynthia, Ongulo Barrack, Awori Mark, Waris Adil
Paediatric Pulmonology Unit, Gertrude's Children's Hospital Nairobi, Kenya.
Paediatric Critical Care Unit, Gertrude's Children's Hospital Nairobi, Kenya.
Respir Med Case Rep. 2021 Oct 26;34:101542. doi: 10.1016/j.rmcr.2021.101542. eCollection 2021.
Paediatric plastic bronchitis (PB) is a rare disease characterized by the presence or expectoration of branching airway casts usually in children with cardiac conditions and allergy. It is thought to be due to obstruction or altered drainage of the lymphatics in those with cardiac conditions. Obstruction can be diffuse and thus fatal if untreated. Less than 600 cases have been described in literature and just one in our region in a patient with sickle cell disease. We present a case of a 7-year-old female with acute symptoms suggestive of a lower respiratory tract infection and left hemithorax opacification and bronchial casts on bronchoscopy.
小儿塑料支气管炎(PB)是一种罕见疾病,其特征是通常在患有心脏疾病和过敏的儿童中出现或咳出分支状气道铸型。据认为,这是由于心脏疾病患者的淋巴管阻塞或引流改变所致。如果不治疗,阻塞可能是弥漫性的,从而危及生命。文献中描述的病例不到600例,而在我们地区,仅1例发生在镰状细胞病患者中。我们报告一例7岁女性患者,有提示下呼吸道感染的急性症状,左半胸混浊,支气管镜检查发现支气管铸型。