Ali Mohamed Daoud, Waiss Amarkak, Onka Behyamet, Mohamed Walid, Allali Nazik, Chat Latifa, El Haddad Siham
University Hospital of Ibn Sina Rabat, Rabat, Morroco.
Glob Pediatr Health. 2021 Nov 30;8:2333794X211051186. doi: 10.1177/2333794X211051186. eCollection 2021.
Pulmonary Arteriovenous Malformations (PAVMs) are structurally abnormal vascular communications between pulmonary arteries and pulmonary veins, which bypass the normal capillary bed and cause a low resistance right-to-left shunt with refractory hypoxemia. Generally, PAVMs were congenital, most commonly associated with (Hereditary hemorrhagic teleangiectasia (HHT). The age of diagnosis is very variable, range neonatal to adulthood, mostly diagnosed in the first 3 decades of life and clinical manifestations occur later in life generally. Here, we report PAVMs discovered incidentally in a 10-years-old child without any known risk factor.
肺动静脉畸形(PAVM)是肺动脉与肺静脉之间结构异常的血管交通,绕过正常毛细血管床,导致低阻力的右向左分流并引起难治性低氧血症。一般来说,PAVM是先天性的,最常见于遗传性出血性毛细血管扩张症(HHT)。诊断年龄差异很大,从新生儿到成年均可发病,大多在生命的前三十年被诊断出来,而临床表现通常在生命后期出现。在此,我们报告一例在一名10岁儿童中偶然发现的PAVM,该儿童无任何已知危险因素。