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伴有边缘性角膜营养不良(结晶样视网膜病变)的比埃蒂氏视网膜色素变性:病例报告

Bietti's tapetoretinal degeneration with marginal corneal dystrophy (crystalline retinopathy): case report.

作者信息

Harrison R J, Acheson R R, Dean-Hart J C

出版信息

Br J Ophthalmol. 1987 Mar;71(3):220-3. doi: 10.1136/bjo.71.3.220.

DOI:10.1136/bjo.71.3.220
PMID:3493804
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1041124/
Abstract

A patient with Bietti's tapetoretinal degeneration and marginal corneal dystrophy is reported on. Refractile deposits found in both the retina and cornea are the most striking feature of this condition. Apart from a slight reduction in left visual acuity there were no visual symptoms. The dark adapted electroretinogram was abnormal. No metabolic disturbance was detected.

摘要

报告了一例患有比埃蒂氏视网膜色素变性和边缘性角膜营养不良的患者。视网膜和角膜中发现的屈光性沉积物是这种疾病最显著的特征。除左眼视力略有下降外,无视觉症状。暗适应视网膜电图异常。未检测到代谢紊乱。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/cf0e32710dc4/brjopthal00613-0059-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/b9c834a97984/brjopthal00613-0058-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/2b82df9ee6f3/brjopthal00613-0058-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/63c7d6079847/brjopthal00613-0059-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/d900f1439996/brjopthal00613-0059-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/cf0e32710dc4/brjopthal00613-0059-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/b9c834a97984/brjopthal00613-0058-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/2b82df9ee6f3/brjopthal00613-0058-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/63c7d6079847/brjopthal00613-0059-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/d900f1439996/brjopthal00613-0059-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5675/1041124/cf0e32710dc4/brjopthal00613-0059-c.jpg

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Bietti's tapetoretinal degeneration with marginal corneal dystrophy (crystalline retinopathy): case report.伴有边缘性角膜营养不良(结晶样视网膜病变)的比埃蒂氏视网膜色素变性:病例报告
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Bietti's tapetoretinal degeneration with marginal corneal dystrophy.伴有边缘性角膜营养不良的比埃蒂氏视网膜色素变性
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Predicting visual acuity in Bietti crystalline dystrophy: evaluation of image parameters.

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Enhancement of staphylococcal virulence for mice by intraperitoneal cortisone acetate, cholesterol and lecithin.腹腔注射醋酸可的松、胆固醇和卵磷脂增强葡萄球菌对小鼠的毒力。
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Evolution of Cellular Inclusions in Bietti's Crystalline Dystrophy.比埃蒂结晶状营养不良中细胞内含物的演变
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Bietti's crystalline dystrophy in Asians: clinical, angiographic and electrophysiological characteristics.亚洲人中的比耶蒂结晶状视网膜变性:临床、血管造影及电生理特征
Int Ophthalmol. 2009 Dec;29(6):459-70. doi: 10.1007/s10792-008-9266-7. Epub 2008 Oct 15.
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Crystalline retinopathy (Bietti's tapetoretinal degeneration without marginal corneal dystrophy).结晶样视网膜病变(无边缘角膜营养不良的比埃蒂毯层视网膜变性)
Am J Ophthalmol. 1981 Nov;92(5):640-6. doi: 10.1016/s0002-9394(14)74655-0.
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The Sjogren-Larsson syndrome.
Arch Ophthalmol. 1968 Sep;80(3):308-16. doi: 10.1001/archopht.1968.00980050310003.
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Bietti's tapetoretinal degeneration with marginal corneal dystrophy.伴有边缘性角膜营养不良的比埃蒂氏视网膜色素变性
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7
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Br J Ophthalmol. 1974 Jan;58(1):3-23. doi: 10.1136/bjo.58.1.3.
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Flecked retina. Appearance secondary to oxalate crystals from methoxyflurane anesthesia.
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Bietti's crystalline fundus dystrophy.比埃蒂结晶状眼底营养不良
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