Pretorius Johannes Jacobus, Hiesgen Juliane, Myburgh Michael, Suleman Farhana E
Department of Diagnostic and Interventional Radiology, University of Pretoria, Department of Radiology, Private Bag X169 Pretoria 0001.
Department of Neurology, University of Pretoria, Private Bag X169 Pretoria 0001.
Radiol Case Rep. 2021 Dec 18;17(3):592-598. doi: 10.1016/j.radcr.2021.11.046. eCollection 2022 Mar.
Behçet's disease is a rare, systemic variable vessel vasculitis mostly seen in patients from the Middle East, Northern Africa and Central Asia. Neuro-Behçet disease (NBD) is often diagnosed in patients with known Behçet's disease who present with neurological symptoms and radiological features of central nervous system involvement. There are very few cases with neuro-Behçet reported from Sub-Saharan Africa in the literature. We report a case of severe parenchymal neuro-Behçet with pseudo-tumoral brainstem lesions in a young male patient of South African origin.
白塞病是一种罕见的全身性可变血管炎，多见于中东、北非和中亚地区的患者。神经白塞病（NBD）通常在患有已知白塞病且出现中枢神经系统受累的神经症状和放射学特征的患者中被诊断出来。文献中报道的来自撒哈拉以南非洲的神经白塞病病例非常少。我们报告一例来自南非的年轻男性患者，患有严重的实质性神经白塞病并伴有假性肿瘤性脑干病变。
