Eye Hospital, Wenzhou Medical University, Wenzhou, Zhejiang Province, People's Republic of China.
BMC Surg. 2022 Jan 8;22(1):9. doi: 10.1186/s12893-021-01459-x.
Bone fibrous dysplasia is a benign disease of bone tissue dysplasia. Vision impairment is the commonest neurological complication of craniofacial fibrous dysplasia. Most of the vision loss caused by craniofacial fibrous dysplasia is usually a gradual process. Very few present with acute visual impairment as described in our case.
We report a patient with fibrous dysplasia presenting rapidly progressive visual loss in the left eye secondary to bone cyst formation. Transnasal endoscopic surgery guided by navigation with drainage and curettage of this bone cyst and orbital decompression resulted in progressive improvement in visual acuity that returned to normal 1 month post-operatively.
In cases with acute visual loss due to fibrous dysplasia, emergency surgical treatment should be considered to preserve vision. In the surgical approach, navigation-guided nasal endoscopic surgery may be preferred because of its advantages.
骨纤维结构不良是骨组织发育不良的良性疾病。视力损害是颅面骨纤维结构不良最常见的神经并发症。颅面骨纤维结构不良引起的大多数视力丧失通常是一个逐渐的过程。像我们描述的这种病例中，很少有急性视力损害的情况。
我们报告了一例纤维结构不良患者，因骨囊肿形成导致左眼视力迅速下降。导航引导下经鼻内镜手术进行引流和刮除该骨囊肿，并进行眶减压术，术后 1 个月视力逐渐恢复正常。
对于纤维结构不良引起的急性视力丧失病例，应考虑紧急手术治疗以保护视力。在手术方法中，导航引导下的鼻内镜手术可能因其优势而被优先考虑。
