Kobayashi Kimihiro, Kuroda Yoshinori, Nakai Shingo, Uchida Tetsuro
Second Department of Surgery, Faculty of Medicine, Yamagata University, 2-2-2 Iida-Nishi, Yamagata, 990-9585, Japan.
Gen Thorac Cardiovasc Surg. 2022 Apr;70(4):390-393. doi: 10.1007/s11748-021-01756-5. Epub 2022 Jan 11.
Autosomal dominant polycystic kidney disease is a systemic disorder associated with cardiovascular complications. However, there are few reports on autosomal dominant polycystic kidney disease-associated aortic dissection. Herein, we present a rare case of a 46-year-old man with autosomal dominant polycystic kidney disease who underwent endovascular repair for acute type B aortic dissection three years after his initial open surgery for acute type A aortic dissection. The postoperative course was uneventful, and he is doing well two years after the endovascular repair. Clinicians should be aware of the potential for occurrence of aortic dissection in patients with autosomal dominant polycystic kidney disease, including the possibility of recurrence.
常染色体显性多囊肾病是一种与心血管并发症相关的全身性疾病。然而，关于常染色体显性多囊肾病相关主动脉夹层的报道较少。在此，我们报告一例罕见病例，一名46岁的常染色体显性多囊肾病男性，在首次接受急性A型主动脉夹层开放手术后三年，因急性B型主动脉夹层接受了血管腔内修复术。术后过程顺利，血管腔内修复术后两年他情况良好。临床医生应意识到常染色体显性多囊肾病患者发生主动脉夹层的可能性，包括复发的可能性。
