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因肠旋转不良而导致的十二指肠前门静脉缺失引起的十二指肠梗阻。

Duodenal obstruction due to missed pre-duodenal portal vein in a patient with intestinal malrotation.

机构信息

Department of Surgery, College of Medicine, Kaduna State University and Barau Dikko Teaching Hospital; Department of Surgery, Epsilon Specialist Hospital, Barnawa, Kaduna, Nigeria.

Department of Surgery, Epsilon Specialist Hospital, Barnawa, Kaduna, Nigeria.

出版信息

Afr J Paediatr Surg. 2022 Apr-Jun;19(2):109-111. doi: 10.4103/ajps.AJPS_146_20.

DOI:10.4103/ajps.AJPS_146_20
PMID:35017382
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8809464/
Abstract

Pre-duodenal portal vein (PDPV) is a rare anomaly and a rare cause of duodenal obstruction (DO), with only a few cases reported in the literature. We present an infant whose bilious vomiting persisted despite having Ladd's procedure for intestinal malrotation due to a missed diagnosis of DO from PDPV that was found at re-exploration. The patient was diagnosed with malrotation and had Ladd's procedure at 12 weeks of age, but bilious vomiting persisted post-operatively. The patient presented to us after 4 weeks, was clinically malnourished and dehydrated, resuscitation was done and re-exploratory laparotomy performed, where an obstructing PDPV was found and a duodeno-duodenostomy was performed anterior to PDPV. However, the patient died on post-operative day 7 probably from severe malnutrition due to delayed diagnosis and absence of parenteral nutrition. We conclude that PDPV may be a cause of DO in infants with malrotation and should be properly sought for during Ladd's procedure for possible bypass surgery if found.

摘要

胃十二指肠前静脉(PDPV)是一种罕见的异常,也是十二指肠梗阻(DO)的罕见原因,文献中仅报道了少数几例。我们报告了一例婴儿,由于术前漏诊 PDPV 导致 DO,尽管已经进行了 Ladd 手术治疗肠旋转不良,但仍持续胆汁性呕吐,在再次探查时发现了该病例。该患者在 12 周龄时因肠旋转不良行 Ladd 手术,但术后仍持续胆汁性呕吐。4 周后,该患者就诊,临床营养不良伴脱水,进行了复苏治疗并进行了剖腹探查术,术中发现 PDPV 梗阻,并在 PDPV 前进行了十二指肠空肠吻合术。然而,该患者术后第 7 天死亡,可能是由于诊断延迟和缺乏肠外营养导致严重营养不良。我们得出结论,PDPV 可能是伴有肠旋转不良的婴儿 DO 的原因,如果发现 PDPV,应在 Ladd 手术时适当寻找,以便进行可能的旁路手术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5c87/8809464/871728ea9887/AJPS-19-109-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5c87/8809464/56e48e29a561/AJPS-19-109-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5c87/8809464/871728ea9887/AJPS-19-109-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5c87/8809464/56e48e29a561/AJPS-19-109-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5c87/8809464/871728ea9887/AJPS-19-109-g002.jpg

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本文引用的文献

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Preduodenal Portal Vein Associated with Duodenal Obstruction of other Etiology: A Case Series.与其他病因导致的十二指肠梗阻相关的十二指肠前门静脉:病例系列
J Neonatal Surg. 2016 Oct 10;5(4):54. doi: 10.21699/jns.v5i4.341. eCollection 2016 Oct-Dec.
2
Duodenal obstruction due to a preduodenal portal vein.十二指肠前门静脉导致的十二指肠梗阻
Afr J Paediatr Surg. 2014 Oct-Dec;11(4):359-61. doi: 10.4103/0189-6725.143176.
3
Preduodenal portal vein: a 3-case series demonstrating varied presentations in infants.十二指肠前门静脉:一项包含3例病例的系列研究,展示了婴儿的不同表现。
J Korean Surg Soc. 2013 Oct;85(4):195-7. doi: 10.4174/jkss.2013.85.4.195. Epub 2013 Sep 30.
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Preduodenal portal vein, malrotation, and high jejunal atresia: a case report.十二指肠门前静脉、旋转不良和高位空肠闭锁:一例报告。
J Pediatr Surg. 2012 Jan;47(1):e27-30. doi: 10.1016/j.jpedsurg.2011.09.059.
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Preduodenal portal vein and malrotation: what causes the obstruction?十二指肠前门静脉与肠旋转不良:梗阻的原因是什么?
Eur J Pediatr Surg. 2008 Jun;18(3):153-5. doi: 10.1055/s-2008-1038647.
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Congenital duodenal obstruction due to a preduodenal portal vein.
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Pre duodenal portal vein as a cause of duodenal obstruction in an adult.
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8
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