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十二指肠前门静脉:两例独特表现及个性化手术治疗策略的病例报告

Preduodenal portal vein: two distinct case reports with unique presentations and tailored surgical management strategies.

作者信息

Elnour Abdelrahman S, Taha Isam, Helali Mohamed, Nugud Faisal

机构信息

National Centre for Pediatric Surgery, Wad Madani, Sudan.

Department of Pediatric Surgery, National Ribat University Hospital, Khartoum, Sudan.

出版信息

J Surg Case Rep. 2024 Dec 26;2025(1):rjae813. doi: 10.1093/jscr/rjae813. eCollection 2025 Jan.

DOI:10.1093/jscr/rjae813
PMID:39726570
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11670779/
Abstract

Preduodenal portal vein (PDPV) is a rare congenital vascular malformation, which was first described by Knight in 1921 as an anomalous vein that lies in front of the duodenum, common bile duct, and hepatic artery instead of beneath them. This abnormal position may result in congenital duodenal obstruction and puts it in danger during operations around this region. PDPV is typically associated with other congenital anomalies, mainly intraabdominal and cardiac ones. The surgical management is usually determined intraoperatively based on evidence that the PDPV is the real cause of obstruction. We report two cases of PDPV each with a different presentation and management approach.

摘要

十二指肠前门静脉(PDPV)是一种罕见的先天性血管畸形,1921年由奈特首次描述为一条异常静脉,它位于十二指肠、胆总管和肝动脉前方而非其下方。这种异常位置可能导致先天性十二指肠梗阻,并在该区域周围的手术中使其处于危险之中。PDPV通常与其他先天性异常相关,主要是腹腔内和心脏方面的异常。手术管理通常在术中根据PDPV是梗阻真正原因的证据来确定。我们报告两例PDPV病例,每个病例都有不同的表现和处理方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/051681d72108/rjae813f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/6323c93e163f/rjae813f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/537bb0d2fa37/rjae813f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/051681d72108/rjae813f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/6323c93e163f/rjae813f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/537bb0d2fa37/rjae813f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b272/11670779/051681d72108/rjae813f3.jpg

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本文引用的文献

1
Congenital duodenal obstruction - Advances in diagnosis, surgical management, and associated controversies.先天性十二指肠梗阻——诊断、手术处理及相关争议的进展。
Semin Pediatr Surg. 2022 Feb;31(1):151140. doi: 10.1016/j.sempedsurg.2022.151140. Epub 2022 Feb 18.
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Duodenal obstruction due to missed pre-duodenal portal vein in a patient with intestinal malrotation.因肠旋转不良而导致的十二指肠前门静脉缺失引起的十二指肠梗阻。
Afr J Paediatr Surg. 2022 Apr-Jun;19(2):109-111. doi: 10.4103/ajps.AJPS_146_20.
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新生儿胆道闭锁合并十二指肠前门静脉:一例报告
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Preduodenal Portal Vein Associated With Intestinal Malrotation and Jejunal Atresia.十二指肠前门静脉伴肠旋转不良和空肠闭锁
Cureus. 2021 Jul 18;13(7):e16467. doi: 10.7759/cureus.16467. eCollection 2021 Jul.
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Surgical Decision Making in Preduodenal Portal Vein: Report of Two Cases in Neonates.十二指肠前门静脉的手术决策:两例新生儿病例报告
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AN ANOMALOUS PORTAL VEIN WITH ITS SURGICAL DANGERS.异常门静脉及其手术风险
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