Frutuoso Luisa, Pereira Ana Marta, Carvalho Lucia, Gonçalves Gil, Nora Mário
General Surgery, Centro Hospitalar de Entre Douro e Vouga, Santa Maria da Feira, PRT.
General Surgery, Champalimaud Foudation, Lisbon, PRT.
Cureus. 2021 Dec 8;13(12):e20258. doi: 10.7759/cureus.20258. eCollection 2021 Dec.
Adenomyomatous hyperplasia is an extremely rare lesion encountered in the ampulla of Vater. Less than 50 cases have been described, most of them with clinical consequences of biliary obstruction, misdiagnosing it as a malignancy. The authors present a concomitant case with a renal tumor, its diagnosis, management, and clinical relevance, as well as a brief revision of the literature. Ampullar and renal tumors were found in a 74-year-old female, in the imagiologic study of a low back pain, in the emergency department. Both were considered malign after further study, and pancreatoduodenectomy with partial nephrectomy was proposed. There is no accurate diagnostic tool to differentiate the benign nature of adenomyomatous hyperplasia and extensive operations are often performed. As an incidental finding in the study of another tumor, this case raises the concern about which and how to treat both tumors, taking into account the morbidity of the respective interventions.
腺肌瘤样增生是一种在 Vater 壶腹极为罕见的病变。已报道的病例少于 50 例,其中大多数伴有胆道梗阻的临床后果,常被误诊为恶性肿瘤。作者介绍了一例合并肾肿瘤的病例,包括其诊断、治疗及临床意义,并对相关文献进行简要回顾。在急诊科对一名 74 岁女性进行腰痛影像学检查时,发现了壶腹肿瘤和肾肿瘤。进一步检查后两者均被认为是恶性的,遂建议行胰十二指肠切除术及部分肾切除术。目前尚无准确的诊断工具来鉴别腺肌瘤样增生的良性性质,且常进行广泛的手术。作为在另一肿瘤研究中的偶然发现,该病例引发了对于如何处理这两种肿瘤以及考虑各自干预措施的发病率的关注。