García-Lechuga Maricela, Vega-Memije María Elisa, Montiel-Rangel Ana Isabel, Torres-González Andres, Rangel-Gamboa Lucia
Departamento de Medicina Interna, Hospital General de Zona No.71 "Benito Coquet," Veracruz, México.
Departamento de Dermatopatología, Hospital General "Dr. Manuel Gea González," Ciudad de México, México.
SAGE Open Med Case Rep. 2022 Jan 19;10:2050313X211072982. doi: 10.1177/2050313X211072982. eCollection 2022.
Pemphigus includes a group of blistering autoimmune diseases that affect the skin and mucosa, characterized by the formation of epidermal bullous and the presence of antibodies against binding proteins. Pemphigus is classified according to clinical presentation, target molecule, and IgG production as pemphigus vulgaris, foliaceous, IgA-pemphigus, and paraneoplastic pemphigus. Thus, the identification of autoantibodies class and site of deposition is mandatory. The gold standard to identify the immune complex deposition is the direct immunofluorescences technique, performed in fresh tissue; unfortunately, this method is unavailable in the regional hospital at the Mexican provinces. Nevertheless, IgG subclass-4 is the prevalence of immunoglobulin in acantholysis. Therefore, this IgG subclass could be detected using IgG4 immunohistochemistry. Because direct immunofluorescences technique is absent in provinces or patients denied a new biopsy to confirm the diagnosis, this work presented pemphigus vulgaris confirmation using the IgG4 immunohistochemistry technique in patients with clinical lesions suggestive of pemphigus vulgaris and intraepidermal blister manifestation in histopathology.
天疱疮是一组影响皮肤和黏膜的水疱性自身免疫性疾病,其特征是表皮水疱形成以及存在针对结合蛋白的抗体。天疱疮根据临床表现、靶分子和IgG产生情况分为寻常型天疱疮、落叶型天疱疮、IgA天疱疮和副肿瘤性天疱疮。因此,确定自身抗体类别和沉积部位是必不可少的。识别免疫复合物沉积的金标准是在新鲜组织中进行的直接免疫荧光技术;不幸的是,墨西哥各省的地区医院没有这种方法。然而,IgG4亚类是棘层松解中免疫球蛋白的主要类型。因此,可以使用IgG4免疫组织化学检测这种IgG亚类。由于各省没有直接免疫荧光技术,或者患者拒绝再次活检以确诊,本研究在具有寻常型天疱疮临床病变且组织病理学表现为表皮内水疱的患者中,使用IgG4免疫组织化学技术对寻常型天疱疮进行确诊。