Department of Otorhinolaryngology-Head and Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia Health Campus, Kota Bharu, Kelantan.
Department of Otorhinolaryngology Head and Neck Surgery, Hospital Sultan Ismail, Johor Bahru.
Gulf J Oncolog. 2021 Sep;1(37):91-94.
Soft tissue sarcoma, especially synovial sarcoma is extremely rare in infancy. Only few cases were reported, and challenges lies in disease eradication and subsequent adjuvant therapy. Due to particularly small size of head and neck region with important structures are in intimate location with each other, surgical resection is very challenging, in order to ensure total disease resection as well as maintaining function and cosmetic outcome post-operatively. We present an uncommon case of synovial sarcoma of infratemporal fossa diagnosed in a 3-month-old infant. Due to extreme age, it poses difficulty to the managing team with regards to surgical intervention and oncological regimes. Keywords : Synovial sarcoma; infratemporal fossa; infant.
软组织肉瘤，尤其是滑膜肉瘤在婴儿中极为罕见。仅有少数病例报道，其治疗难点在于彻底清除肿瘤和后续辅助治疗。由于头颈部区域特别小，且重要结构之间位置毗邻，因此手术切除极具挑战性，既要确保肿瘤完全切除，又要保证术后功能和美容效果。我们报告了一例罕见的婴儿颞下窝滑膜肉瘤病例。由于患儿年龄极小，这给治疗团队在手术干预和肿瘤治疗方案方面带来了困难。
滑膜肉瘤；颞下窝；婴儿
