Center for Diagnostic and Therapeutic Endoscopy, Keio University School of Medicine, Japan.
Department of Internal Medicine, Kensei Hospital, Japan.
Intern Med. 2022 Sep 1;61(17):2607-2611. doi: 10.2169/internalmedicine.8939-21. Epub 2022 Feb 19.
Chronic enteropathy associated with solute carrier organic anion transporter family, member 2A1 (SLCO2A1) (CEAS) is a rare autosomal recessive hereditary disease characterized by chronic persistent anemia and hypoproteinemia. Its diagnosis typically requires a genetic analysis. The efficacy of immunohistochemical staining with SLCO2A1 polyclonal antibody as a pre-diagnostic tool for CEAS has been previously reported. We herein report a patient with CEAS in whom immunohistochemical staining confirmed SLCO2A1 protein expression. The immunopositive results may have been due to nonsense-mediated RNA decay. As immunohistochemical staining of SLCO2A1 protein may show immunopositive results, a genetic analysis should also be performed when CEAS is strongly clinically suspected.
常染色体隐性遗传的溶质载体有机阴离子转运家族成员 2A1 相关慢性肠病(CEAS)是一种罕见的遗传性疾病,其特征为慢性持续性贫血和低蛋白血症。其诊断通常需要进行基因分析。先前有报道称,SLCO2A1 多克隆抗体的免疫组化染色作为 CEAS 的一种诊断前工具具有一定的效果。本文报道了一例 CEAS 患者,免疫组化染色证实了 SLCO2A1 蛋白的表达。免疫阳性结果可能是由于无义介导的 RNA 降解所致。由于 SLCO2A1 蛋白的免疫组化染色可能显示免疫阳性结果,因此在强烈怀疑 CEAS 时,还应进行基因分析。