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右心房磷酸甘油酯晶体沉积病所致的严重功能性三尖瓣狭窄

Severe Functional Tricuspid Stenosis Due to Phosphoglyceride Crystal Deposition Disease in Right Atrium.

作者信息

Takeuchi Kimikazu, Tanaka Hidekazu, Kawamori Hiroyuki, Ohta Eri, Suzuki Makiko, Shimoura Hiroyuki, Izawa Yu, Kodama Yoshinori, Hirata Ken-Ichi

机构信息

Division of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of Medicine, Kobe, Japan.

Department of Cardiology, Kakogawa Central City Hospital, Kakogawa, Japan.

出版信息

JACC Case Rep. 2022 Feb 16;4(4):230-235. doi: 10.1016/j.jaccas.2021.09.024.

DOI:10.1016/j.jaccas.2021.09.024
PMID:35199022
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8855130/
Abstract

This case report concerns a 72-year-old-female with severe functional tricuspid stenosis due to phosphoglyceride crystal deposition disease and a history of atrial septum closure and tricuspid valvuloplasty. Phosphoglyceride crystal deposition disease is extremely rare, and percutaneous transcatheter biopsy under intracardiac echocardiographic guidance proved to be useful for its diagnosis. ().

摘要

本病例报告涉及一名72岁女性,因磷酸甘油酯晶体沉积病导致严重功能性三尖瓣狭窄,并有房间隔封堵和三尖瓣成形术病史。磷酸甘油酯晶体沉积病极为罕见,经心腔内超声心动图引导下的经皮经导管活检对其诊断很有用。()

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/ba4cba0d0b58/gr9.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/a3a1a2ba890c/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/dd1ef1f7fb50/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/de9449cc21bb/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/b3a20f68026e/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/8372bb2562ce/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/7e34b1ea3ff9/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/cb0150a151cc/gr6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/4aac3d080b6d/gr7.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/9d1b919525ca/gr8.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/ba4cba0d0b58/gr9.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/a3a1a2ba890c/fx1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/dd1ef1f7fb50/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/de9449cc21bb/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/b3a20f68026e/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/8372bb2562ce/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/7e34b1ea3ff9/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/cb0150a151cc/gr6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/4aac3d080b6d/gr7.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/9d1b919525ca/gr8.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/ba4cba0d0b58/gr9.jpg

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本文引用的文献

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Complete Resection of Phosphoglyceride Crystal Deposition Disease After Cardiac Surgery.心脏手术后磷酸甘油酯晶体沉积病的完全切除。
Ann Thorac Surg. 2021 May;111(5):e315-e317. doi: 10.1016/j.athoracsur.2020.07.099. Epub 2020 Nov 2.
2
Phosphoglyceride (PG) crystal deposition disease: a novel acquired disease in which PG crystals are deposited in injured soft tissue and bone with phospholipid metabolism disturbance.磷酸甘油酯(PG)晶体沉积病:一种新型获得性疾病,其中PG晶体沉积于伴有磷脂代谢紊乱的受损软组织和骨骼中。
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Phosphoglyceride crystal deposition disease.
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Solving the Diagnostic Challenge of Right Atrial Mass.解决右心房肿块的诊断难题
JACC Case Rep. 2022 Feb 16;4(4):236-238. doi: 10.1016/j.jaccas.2022.01.003.
磷酸甘油酯晶体沉积病
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Unusual huge intramuscular granuloma with calcium phosphate crystal deposition in the buttock.
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