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右心房磷酸甘油酯晶体沉积病所致的严重功能性三尖瓣狭窄

Severe Functional Tricuspid Stenosis Due to Phosphoglyceride Crystal Deposition Disease in Right Atrium.

作者信息

Takeuchi Kimikazu, Tanaka Hidekazu, Kawamori Hiroyuki, Ohta Eri, Suzuki Makiko, Shimoura Hiroyuki, Izawa Yu, Kodama Yoshinori, Hirata Ken-Ichi

机构信息

Division of Cardiovascular Medicine, Department of Internal Medicine, Kobe University Graduate School of Medicine, Kobe, Japan.

Department of Cardiology, Kakogawa Central City Hospital, Kakogawa, Japan.

出版信息

JACC Case Rep. 2022 Feb 16;4(4):230-235. doi: 10.1016/j.jaccas.2021.09.024.

Abstract

This case report concerns a 72-year-old-female with severe functional tricuspid stenosis due to phosphoglyceride crystal deposition disease and a history of atrial septum closure and tricuspid valvuloplasty. Phosphoglyceride crystal deposition disease is extremely rare, and percutaneous transcatheter biopsy under intracardiac echocardiographic guidance proved to be useful for its diagnosis. ().

摘要

本病例报告涉及一名72岁女性,因磷酸甘油酯晶体沉积病导致严重功能性三尖瓣狭窄,并有房间隔封堵和三尖瓣成形术病史。磷酸甘油酯晶体沉积病极为罕见,经心腔内超声心动图引导下的经皮经导管活检对其诊断很有用。()

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d9cd/8855130/a3a1a2ba890c/fx1.jpg

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