Cong Cung-Van, Ly Tran-Thi, Duc Nguyen Minh
Department of Radiology, National Lung Hospital, Ha Noi, Vietnam.
Center of Training and Direction of Healthcare Activities, National Lung Hospital, Ha Noi, Vietnam.
Radiol Case Rep. 2022 Feb 21;17(4):1345-1353. doi: 10.1016/j.radcr.2022.01.082. eCollection 2022 Apr.
Sequestration is a congenital abnormality that can occur in both children and adults. The clinical presentation often manifests as recurrent pneumonia throughout the lifetime of the patient. Pathologically, sequestration is a disorganized region of lung parenchyma without a normal pulmonary artery and with no interconnecting air passage (ie, it is isolated from the bronchi and pulmonary arteries). Sequestration can be either intralobar or extralobar and is usually supplied with blood from an anomalous vessel originating from the thoracic aorta or abdominal aorta (big circulation/systemic circulation), which is one of the mandatory criteria for diagnosing sequestration. CT angiography or catheter angiography can assist in identifying the anomalous vessel both for diagnosis and surgical resection. We present a rare case of intralobar sequestration with the distinction of being supplied with blood from the abdominal vena cava, as confirmed by CT angiography, surgery, and postoperative pathology. It is hoped that this study will contribute to the literature by introducing a rare case of congenital lung abnormality and pulmonary vascular malformation.
肺隔离症是一种先天性异常，可发生于儿童和成人。临床表现通常为患者一生中反复发生肺炎。病理上，肺隔离症是肺实质的一个结构紊乱区域，没有正常的肺动脉且没有相互连通的气道（即它与支气管和肺动脉隔离）。肺隔离症可分为叶内型或叶外型，通常由起源于胸主动脉或腹主动脉（大循环/体循环）的异常血管供血，这是诊断肺隔离症的必备标准之一。CT血管造影或导管血管造影有助于识别异常血管，用于诊断和手术切除。我们报告一例罕见的叶内型肺隔离症，经CT血管造影、手术及术后病理证实，其供血血管为腔静脉。希望本研究通过介绍一例罕见的先天性肺异常和肺血管畸形病例，为相关文献做出贡献。
