Daviskiba Sydney, Shuman Hannah, Ayyash Mariam, Vadlamudi Gayathri, Smietana Stefan, Goyert Gregory
Wayne State University School of Medicine, Detroit, MI, United States of America.
Department of Obstetrics and Gynecology, Henry Ford Hospital, Detroit, MI, United States of America.
Case Rep Womens Health. 2022 Mar 9;34:e00403. doi: 10.1016/j.crwh.2022.e00403. eCollection 2022 Apr.
Blue rubber bleb nevus syndrome (BRBNS) is a rare vascular disorder characterized by recurrent, multifocal venous malformations throughout the skin, soft tissue, and numerous internal organs. Pregnant women with BRBNS are at high risk of morbidity and mortality, and thus their care requires careful planning and surveillance. This report highlights the case of a 21-year-old woman, gravida 1, para 0, with BRBNS who was cared for by a multidisciplinary team of providers in obstetrics, maternal-fetal medicine, obstetric anesthesia, hematology, dermatology, gastroenterology, and otorhinolaryngology. The report provides a comprehensive guide to the multidisciplinary management of pregnancy and delivery for patients with BRBNS.
蓝色橡皮疱痣综合征(BRBNS)是一种罕见的血管疾病,其特征是在皮肤、软组织和许多内部器官中反复出现多灶性静脉畸形。患有BRBNS的孕妇有很高的发病和死亡风险,因此对她们的护理需要精心规划和监测。本报告重点介绍了一名21岁、孕1产0、患有BRBNS的女性病例,她由产科、母胎医学、产科麻醉、血液学、皮肤科、胃肠病学和耳鼻咽喉科的多学科医疗团队进行护理。该报告为BRBNS患者的妊娠和分娩多学科管理提供了全面指南。