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另一个福尔摩斯之谜:正中弓状韧带综合征解释的腹痛。

Another Sherlock Holmes Mystery: Abdominal Pain Explained by Median Arcuate Ligament Syndrome.

机构信息

Texas Tech University Health Sciences Center El Paso, TX, USA.

出版信息

J Investig Med High Impact Case Rep. 2022 Jan-Dec;10:23247096221084911. doi: 10.1177/23247096221084911.

DOI:10.1177/23247096221084911
PMID:35313774
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8948318/
Abstract

Median arcuate ligament syndrome (MALS), also known as celiac artery compression syndrome, is a rare gastrointestinal condition with an estimated incidence of 2 per 100 000 population. Predominantly in female patients, this syndrome is characterized by the compression of the celiac artery at its origin from the aorta by the median arcuate ligament, which at the same time is entrapping the celiac plexus, causing upper abdominal pain, notably postprandial pain, as well as nausea, vomiting, food aversion, and weight loss. We present a case of abdominal pain secondary to MALS that was appropriately diagnosed after requiring narcotic medication, which responded to surgical therapy.

摘要

正中弓状韧带综合征(MALS),又称腹腔动脉压迫综合征,是一种罕见的胃肠道疾病,估计发病率为每 10 万人中有 2 例。这种综合征主要发生在女性患者中,其特征是腹主动脉起源处的正中弓状韧带压迫腹腔动脉,同时压迫腹腔丛,导致上腹痛,特别是餐后痛,以及恶心、呕吐、厌食和体重减轻。我们报告了一例因 MALS 引起的腹痛病例,在需要使用麻醉药物后得到了适当的诊断,并对其进行了手术治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/44e327fc028a/10.1177_23247096221084911-fig4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/f494ab6c800a/10.1177_23247096221084911-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/1a59ff1a510b/10.1177_23247096221084911-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/a8dbb8f1ffe9/10.1177_23247096221084911-fig3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/44e327fc028a/10.1177_23247096221084911-fig4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/f494ab6c800a/10.1177_23247096221084911-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/1a59ff1a510b/10.1177_23247096221084911-fig2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/a8dbb8f1ffe9/10.1177_23247096221084911-fig3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d91f/8948318/44e327fc028a/10.1177_23247096221084911-fig4.jpg

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