Ros P R, Olmsted W W, Dachman A H, Goodman Z D, Ishak K G, Hartman D S
Radiology. 1986 Oct;161(1):141-5. doi: 10.1148/radiology.161.1.3532179.
Undifferentiated (embryonal) sarcoma (UES) is an uncommon malignant mesenchymal hepatic tumor that occurs in older children and young adults. Fourteen cases are correlated with radiologic and pathologic findings. Radiologic findings reflect the spectrum of solid to cystic appearances observed in the gross specimens. Sonography typically demonstrates a large mass that may be predominantly solid with many small anechoic spaces or may be cystic. Computed tomography reveals a hypodense mass with hyperdense septa of variable thickness and a dense peripheral rim corresponding to the fibrous pseudocapsule of the tumor. Angiographically, UES is usually hypovascular with tumoral vessels, although hypervascular and avascular patterns occur. Prognosis of UES is poor, with a median survival of less than 1 year. Radiologists should be familiar with this malignant tumor since it may present as a large cystic hepatic mass, suggestive of a benign lesion.
未分化(胚胎性)肉瘤(UES)是一种罕见的发生于大龄儿童和青年成人的恶性间质性肝脏肿瘤。14例病例与放射学和病理学表现相关。放射学表现反映了大体标本中所见的从实性到囊性的外观范围。超声检查通常显示一个大肿块,可能主要为实性,有许多小无回声区,也可能为囊性。计算机断层扫描显示一个低密度肿块,有厚度不一的高密度间隔以及对应肿瘤纤维假包膜的致密周边环。血管造影显示,UES通常血管较少,有肿瘤血管,不过也会出现血管丰富和无血管的情况。UES的预后较差,中位生存期不到1年。放射科医生应熟悉这种恶性肿瘤,因为它可能表现为一个大的囊性肝脏肿块,提示为良性病变。