Martí-Bonmatí L, Ferrer D, Menor F, Galant J
Department of Diagnostic Radiology, Hospital Dr Peset, Valencia, Spain.
Abdom Imaging. 1993;18(2):176-9. doi: 10.1007/BF00198058.
Hepatic undifferentiated mesenchymal sarcoma is a rare pediatric malignant neoplasm. We present three children, aged 7, 8, and 12 years, with this tumor. Clinical presentation was abdominal pain, palpable mass, asthenia, anorexia, and weight loss. One had jaundice. All three lesions were detected on ultrasound (US), computed tomography (CT), and magnetic resonance imaging (MRI). MRI localized the lesions more accurately than the other methods, with good resectability correlation. On MRI, these tumors were markedly hyperintense on long TR/TE spin-echo (SE) and short-time inversion recovery (STIR) sequences. This was due to the cystic areas with myxoid material and necrosis. The internal separations were hypointense on these sequences. On short TR/TE SE sequences the lesions presented a fibrous pseudocapsule (two cases), and internal hyperintense areas representing hemorrhage (two cases). MRI also detected vascular invasion (one case), biliary obstruction (one case), and hilar adenopathies (one case). The combination of hemorrhage (hyperintense on short TR/TE SE) and cystic or myxoid components (markedly hyperintense on long TR/TE SE and STIR sequences) is common in this tumor.
肝未分化间叶肉瘤是一种罕见的儿童恶性肿瘤。我们报告了三名患有这种肿瘤的儿童,年龄分别为7岁、8岁和12岁。临床表现为腹痛、可触及肿块、乏力、厌食和体重减轻。其中一人有黄疸。所有三个病变均通过超声(US)、计算机断层扫描(CT)和磁共振成像(MRI)检测到。MRI比其他方法更准确地定位病变,与良好的可切除性相关。在MRI上,这些肿瘤在长TR/TE自旋回波(SE)和短时反转恢复(STIR)序列上呈明显高信号。这是由于含有黏液样物质和坏死的囊性区域所致。这些序列上内部间隔呈低信号。在短TR/TE SE序列上,病变呈现纤维性假包膜(2例),内部高信号区域代表出血(2例)。MRI还检测到血管侵犯(1例)、胆管梗阻(1例)和肝门淋巴结肿大(1例)。出血(在短TR/TE SE上呈高信号)和囊性或黏液样成分(在长TR/TE SE和STIR序列上明显高信号)的组合在这种肿瘤中很常见。