Stanley P, Hall T R, Woolley M M, Diament M J, Gilsanz V, Miller J H
AJR Am J Roentgenol. 1986 Nov;147(5):1035-9. doi: 10.2214/ajr.147.5.1035.
Mesenchymal hamartomas of the liver usually present within the first 2 years of life. Abdominal enlargement and respiratory distress are the most common presenting features. Pathologically, the lesion is composed of large cysts separated by septations. Review of sonograms and CT scans in nine patients shows that a large, predominantly cystic mass with internal septae is characteristic of the tumor. Angiography shows peripheral hypervascularity with a septated avascular center. A confident preoperative diagnosis of mesenchymal hamartoma based on these features is possible.
肝脏间叶性错构瘤通常在出生后的头两年内出现。腹部膨隆和呼吸窘迫是最常见的临床表现。病理上，病变由被分隔开的大囊肿组成。对9例患者的超声和CT扫描回顾显示，具有内部间隔的大的、以囊性为主的肿块是该肿瘤的特征。血管造影显示周边血管增多，中央为无血管的分隔区。基于这些特征在术前做出肝脏间叶性错构瘤的准确诊断是可能的。
