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1型糖尿病合并糖尿病酮症酸中毒患儿的渗透性脱髓鞘综合征

Pediatric osmotic demyelination syndrome in a case of type 1 diabetes mellitus with diabetic ketoacidosis.

作者信息

Chaudhary Ashlesha, Chaudhary Aashutosh, Yadav Radhay Shyam, Shrestha Yashaswi, Shah Ritu

机构信息

Nepal Medical College and Teaching Hospital Kathmandu Nepal.

Kathmandu University School of Medical Sciences Dhulikhel, Kavreplanchowk Nepal.

出版信息

Clin Case Rep. 2022 Mar 19;10(3):e05584. doi: 10.1002/ccr3.5584. eCollection 2022 Mar.

DOI:10.1002/ccr3.5584
PMID:35340640
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8934147/
Abstract

Cautious treatment of hyponatremia in diabetic ketoacidosis is necessary in order to avoid the development of osmotic demyelination syndrome which is a demyelinating disorder. Individualized supportive therapy would be fruitful for the management of such cases but there is a need for larger studies to guide the management.

摘要

谨慎治疗糖尿病酮症酸中毒中的低钠血症是必要的,以避免发生渗透性脱髓鞘综合征,这是一种脱髓鞘疾病。个体化支持治疗对此类病例的管理可能有效,但需要更大规模的研究来指导管理。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b64/8934147/bfb77d43f5ce/CCR3-10-e05584-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b64/8934147/bfb77d43f5ce/CCR3-10-e05584-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b64/8934147/bfb77d43f5ce/CCR3-10-e05584-g001.jpg

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本文引用的文献

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2
Therapeutic Effect of Steroids in Osmotic Demyelination of Infancy.类固醇对婴儿渗透性脱髓鞘的治疗作用。
Child Neurol Open. 2018 Apr 15;5:2329048X18770576. doi: 10.1177/2329048X18770576. eCollection 2018.
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Osmotic demyelination syndrome: plasmapheresis versus intravenous immunoglobulin?渗透性脱髓鞘综合征:血浆置换与静脉注射免疫球蛋白的比较?
Intern Emerg Med. 2017 Feb;12(1):123-126. doi: 10.1007/s11739-016-1452-4. Epub 2016 Apr 18.
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Osmotic demyelination syndrome associated with hypophosphataemia: 2 cases and a review of literature.低磷血症相关性渗透性髓鞘溶解综合征:2 例病例报告及文献复习。
Acta Paediatr. 2013 Apr;102(4):e164-8. doi: 10.1111/apa.12143. Epub 2013 Jan 21.
5
Relowering of serum na for osmotic demyelinating syndrome.血清钠再次降低导致渗透性脱髓鞘综合征。
Case Rep Neurol Med. 2012;2012:704639. doi: 10.1155/2012/704639. Epub 2012 Jun 28.
6
Osmotic demyelination syndrome: variable clinical and radiologic response to intravenous immunoglobulin therapy.渗透性脱髓鞘综合征:静脉注射免疫球蛋白治疗的临床和影像学反应各异。
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