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肠系膜孤立性纤维瘤病例报告及文献综述:“千载难逢”

Case report of mesenteric solitary fibrous tumour and review of the literature: 'once in a blue moon'.

作者信息

Nicotera Antonella, Canova Gualtiero, Bono Dario, Gattoni Luca, Zago Marcello, Bonomo Luca Domenico

机构信息

Department of General Surgery, SS. Pietro e Paolo Hospital, ASL VC, via A.F. Ilorini Mo 20, 13011, Borgosesia (VC), Italy.

出版信息

J Surg Case Rep. 2022 Mar 26;2022(3):rjac097. doi: 10.1093/jscr/rjac097. eCollection 2022 Mar.

Abstract

Solitary fibrous tumour (SFT) is a rare mesenchymal tumour, usually originating from the serous surfaces, typically of the pleura and pericardium. However, it can also have localizations in soft tissues and visceral organs. We report the case of a 79-year-old woman affected by mesenteric SFT, localized in the sigmoid colon. We performed open excision of the abovementioned mass en-bloc with the sigmoid colon and left adnexal tissues. Pathological examination of surgical specimen revealed a diagnosis of SFT CD34+, high-risk of metastases. Mesenteric SFTs are even rarer forms of SFT and may be asymptomatic or cause intestinal occlusion. There is no consensus on the management of this tumour. Radical surgical excision is the only curative treatment, while adjuvant therapies are indicated in case of advanced disease. Due to the high metastatic risk of malignant forms, a long follow-up is mandatory in these cases.

摘要

孤立性纤维瘤(SFT)是一种罕见的间叶组织肿瘤,通常起源于浆膜表面,典型的是胸膜和心包。然而,它也可发生于软组织和内脏器官。我们报告一例79岁女性患有肠系膜SFT,位于乙状结肠。我们对上述肿物连同乙状结肠和左侧附件组织进行了整块开放性切除。手术标本的病理检查显示诊断为CD34+的SFT,转移风险高。肠系膜SFT是SFT中更为罕见的类型,可能无症状或导致肠梗阻。对于这种肿瘤的治疗尚无共识。根治性手术切除是唯一的治愈性治疗方法,而对于晚期疾病则需进行辅助治疗。由于恶性形式的转移风险高,这些病例必须进行长期随访。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/92ae/8963141/77ecac7169b3/rjac097f1.jpg

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