Makary Joshua, Rathore Prem
The University of Sydney, Australia.
Campbelltown Hospital, Australia.
Urol Case Rep. 2022 Mar 25;43:102062. doi: 10.1016/j.eucr.2022.102062. eCollection 2022 Jul.
In this report we describe the clinical journey of a 62-year-old male that presented with acute kidney injury secondary to Erdheim-Chester disease, a non-Langerhans variant of histiocytosis rarely encountered by urological surgeons. ECD can uncommonly cause acute renal failure and management includes decompression of the collecting system. A multi-disciplinary approach is required to facilitate adequate investigation to determine the specific ECD subtype and most appropriate treatment options, particularly as the available targeted therapies have only recently been utilised.
在本报告中，我们描述了一名62岁男性的临床病程，该患者因 Erdheim-Chester 病继发急性肾损伤，这是一种组织细胞增多症的非朗格汉斯变种，泌尿外科医生很少遇到。Erdheim-Chester 病罕见地可导致急性肾衰竭，治疗包括集合系统减压。需要采取多学科方法以便进行充分的检查，以确定特定的 Erdheim-Chester 病亚型和最合适的治疗方案，特别是因为可用的靶向治疗最近才开始应用。
