Division of Cardiothoracic Surgery, Congenital Heart Disease Center, Nara Medical University, Nara, Japan.
J Card Surg. 2022 Jul;37(7):2124-2126. doi: 10.1111/jocs.16488. Epub 2022 Apr 5.
A complex and rare form of double outlet right ventricle needs careful attention when choosing the optimal strategy for repair.
To point out retrospectively what could have been done differently in our unique patient.
Primary repair was arranged in a neonate with double outlet right ventricle (of a non-committed ventricular septal defect type and lack of the outlet septum between the semilunar valves) with right aortic arch and dextro-malposition of great arteries.
We managed to achieve intraventricular rerouting via a right ventricular incision concomitantly with the arterial switch maneuver. The patient is doing well with an excellent hemodynamic status.
We considered that the radical approach we chose appeared to be sensible in this particular patient, although some other options could have been available.
复杂且罕见的右心室双出口需要在选择最佳修复策略时仔细考虑。
回顾性指出我们独特患者中可能存在的不同之处。
对一名患有右心室双出口（非约束性室间隔缺损型，且半月瓣之间缺乏流出隔）、右位主动脉弓和大动脉转位的新生儿进行了一期修复。
我们成功地通过右心室切口同时进行动脉切换操作实现了室内再通。患者情况良好，血流动力学状态极佳。
我们认为，虽然可能有其他选择，但我们选择的激进方法在这种特殊患者中似乎是合理的。
