左侧颊部硬化性横纹肌肉瘤及孤立游离皮瓣供区转移。
Left cheek sclerosing rhabdomyosarcoma and development of isolated free flap donor site metastasis.
机构信息
Department of Medical Oncology, Chris O'Brien Lifehouse, Camperdown, New South Wales, Australia.
The University of Sydney, Sydney, New South Wales, Australia.
出版信息
BMJ Case Rep. 2022 Apr 7;15(4):e248390. doi: 10.1136/bcr-2021-248390.
Rhabdomyosarcoma is a rare mesenchymal malignancy with four different morphological subtypes: alveolar, embryonal, pleomorphic and spindle cell/sclerosing. It is the most common soft tissue sarcoma of children and adolescents but occurs less commonly in adults. We describe a male patient in his 20s with sclerosing rhabdomyosarcoma of the left cheek who developed an isolated free flap donor site metastasis in the first instance but subsequently progressed with bilateral pulmonary metastases. Multidisciplinary team involvement in a sarcoma specialist centre is essential and collaboration between the pathologist, radiologist, head and neck surgeon, orthopaedic surgeon, radiation oncologist and medical oncologist were integral in providing optimal management in this patient. Furthermore, this case report highlights this phenomenon of implantation metastasis in a patient with rhabdomyosarcoma, and emphasises the importance of surgical barriers between the resection and reconstruction teams in an oncological case.
横纹肌肉瘤是一种罕见的间叶性恶性肿瘤，有四种不同的形态亚型：肺泡状、胚胎性、多形性和梭形/硬化性。它是儿童和青少年中最常见的软组织肉瘤，但在成人中较少见。我们描述了一名 20 多岁的男性患者，其左侧脸颊患有硬化性横纹肌肉瘤，最初出现孤立的游离皮瓣供区转移，随后双侧肺部转移进展。肉瘤专家中心的多学科团队参与至关重要，病理学家、放射科医生、头颈外科医生、矫形外科医生、放射肿瘤学家和肿瘤内科医生之间的合作对于为该患者提供最佳治疗至关重要。此外，本病例报告强调了横纹肌肉瘤患者中这种种植转移现象，并强调了在肿瘤病例中，切除和重建团队之间手术屏障的重要性。
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