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An analysis of sex differences in pulmonary arteriovenous malformation presentation, complications and management in a large, multinational registry of patients with hereditary haemorrhagic telangiectasia.在一个大型跨国遗传性出血性毛细血管扩张症患者登记处中,对肺动静脉畸形的表现、并发症及治疗方面的性别差异进行分析。
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本文引用的文献

1
Brain Vascular Malformation Consortium: Overview, Progress and Future Directions.脑血管畸形联盟:概述、进展与未来方向。
J Rare Disord. 2013 Apr 1;1(1):5.
2
Pulmonary vascular complications of hereditary haemorrhagic telangiectasia.遗传性出血性毛细血管扩张症的肺血管并发症
Curr Opin Pulm Med. 2014 Sep;20(5):421-8. doi: 10.1097/MCP.0000000000000076.
3
A long diagnostic delay in patients with Hereditary Haemorrhagic Telangiectasia: a questionnaire-based retrospective study.遗传性出血性毛细血管扩张症患者的诊断延迟时间长:基于问卷调查的回顾性研究。
Orphanet J Rare Dis. 2012 Jun 7;7:33. doi: 10.1186/1750-1172-7-33.
4
International guidelines for the diagnosis and management of hereditary haemorrhagic telangiectasia.国际遗传性出血性毛细血管扩张症诊断和管理指南。
J Med Genet. 2011 Feb;48(2):73-87. doi: 10.1136/jmg.2009.069013. Epub 2009 Jun 23.
5
The pulmonary vascular complications of hereditary haemorrhagic telangiectasia.遗传性出血性毛细血管扩张症的肺血管并发症
Eur Respir J. 2009 May;33(5):1186-94. doi: 10.1183/09031936.00061308.
6
Primary determinants of ischaemic stroke/brain abscess risks are independent of severity of pulmonary arteriovenous malformations in hereditary haemorrhagic telangiectasia.缺血性中风/脑脓肿风险的主要决定因素与遗传性出血性毛细血管扩张症中肺动静脉畸形的严重程度无关。
Thorax. 2008 Mar;63(3):259-66. doi: 10.1136/thx.2007.087452. Epub 2007 Nov 2.
7
Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (rendu-osler disease).遗传性出血性毛细血管扩张症(伦杜-奥斯勒病)的肺血管表现
Respiration. 2007;74(4):361-78. doi: 10.1159/000103205.
8
Diagnostic criteria for hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber syndrome).遗传性出血性毛细血管扩张症(伦杜-奥斯勒-韦伯综合征)的诊断标准。
Am J Med Genet. 2000 Mar 6;91(1):66-7. doi: 10.1002/(sici)1096-8628(20000306)91:1<66::aid-ajmg12>3.0.co;2-p.
9
Pulmonary arteriovenous malformations. A state of the art review.肺动静脉畸形。一篇前沿综述。
Am J Respir Crit Care Med. 1998 Aug;158(2):643-61. doi: 10.1164/ajrccm.158.2.9711041.
10
Pulmonary arteriovenous malformations: techniques and long-term outcome of embolotherapy.肺动静脉畸形:栓塞治疗技术及长期疗效
Radiology. 1988 Dec;169(3):663-9. doi: 10.1148/radiology.169.3.3186989.

Neurovascular Complications and Pulmonary Arteriovenous Malformation Feeding Artery Size.

作者信息

Ananiadis Theodora, Faughnan Marie E, Clark Dewi, Prabhudesai Vikram, Kim Helen, Lawton Michael T, Vozoris Nicholas T

机构信息

University of Western Ontario London, Ontario, Canada.

University of Toronto Toronto, Ontario, Canada.

出版信息

Ann Am Thorac Soc. 2022 Aug;19(8):1432-1435. doi: 10.1513/AnnalsATS.202202-130RL.

DOI:10.1513/AnnalsATS.202202-130RL
PMID:35442860
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9353961/
Abstract
摘要