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[2022版肝豆状核变性诊断与治疗指南解读]

[Interpretation of the 2022 edition guidelines for hepatolenticular degeneration diagnosis and treatment].

作者信息

Hou W, Zheng S J, Duan Zhongping

机构信息

The First Department of the Liver Disease Center, Beijing You'an Hospital, Capital Medical University, Beijing 100069, China.

The Fourth Department of the Liver Disease Center, Beijing You'an Hospital, Capital Medical University, Beijing 100069, China.

出版信息

Zhonghua Gan Zang Bing Za Zhi. 2022 Mar 20;30(3):276-278. doi: 10.3760/cma.j.cn501113-20220211-00065.

DOI:10.3760/cma.j.cn501113-20220211-00065
PMID:35462482
Abstract

In order to help liver disease-related clinicians make rational decisions, the Inherited and Metabolic Liver Disease Cooperative Group of Hepatology Branch of Chinese Medical Association released the 2022 edition guidelines for hepatolenticular degeneration diagnosis and treatment. This article introduces the ten highlights of this guideline from the aspects of epidemiology, pathogenesis, clinical characteristics, laboratory tests, diagnosis, treatment, monitoring, and so forth, with practicality and operability as prominent features.

摘要

为帮助肝脏疾病相关临床医生做出合理决策,中华医学会肝病学分会遗传和代谢性肝病协作组发布了《2022版肝豆状核变性诊断和治疗指南》。本文从流行病学、发病机制、临床特点、实验室检查、诊断、治疗、监测等方面介绍该指南的十大亮点,突出实用性和可操作性。

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[Interpretation of the 2022 edition guidelines for hepatolenticular degeneration diagnosis and treatment].[2022版肝豆状核变性诊断与治疗指南解读]
Zhonghua Gan Zang Bing Za Zhi. 2022 Mar 20;30(3):276-278. doi: 10.3760/cma.j.cn501113-20220211-00065.
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[Guidelines for the diagnosis and treatment of hepatolenticular degeneration (2022 edition)].肝豆状核变性诊断和治疗指南(2022年版)
Zhonghua Gan Zang Bing Za Zhi. 2022 Jan 20;30(1):9-20. doi: 10.3760/cma.j.cn501113-20211217-00603.
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[An interpretation of the British Association for the Study of the Liver practice guideline for the evaluation and treatment of hepatolenticular degeneration].[英国肝脏研究协会肝豆状核变性评估与治疗实践指南解读]
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Wilson's Disease in Children: A Position Paper by the Hepatology Committee of the European Society for Paediatric Gastroenterology, Hepatology and Nutrition.儿童威尔逊氏病:欧洲儿科胃肠病学、肝病学和营养学会肝病学委员会立场文件
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Orthotopic liver transplantation for acute fulminant Wilson disease.
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