多种先天性内脏异常作为肺动脉高压的罕见病因
Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension.
作者信息
Rabiee Parham, Saedi Sedigheh
机构信息
Radiology Department, Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Cardiology and Adult Congenital Heart Disease Department, Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Vali-asr Ave, Adjacent to Mellat Park, 1995614331, Tehran, Iran.
出版信息
Egypt Heart J. 2022 Apr 28;74(1):34. doi: 10.1186/s43044-022-00273-x.
BACKGROUND
Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group.
CASE PRESENTATION
Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension.
CONCLUSIONS
Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options.
背景
肺动脉高压（PAH）是一种罕见的进行性疾病。PAH由多种病理情况引起，但在很多情况下病因仍不明确，患者被归类为特发性组。
病例报告
在此，我们报告一名患有罕见先天性内脏异常并伴有严重肺动脉高压的年轻女性。
结论
肺动脉高压是一种复杂的疾病。有必要寻找导致肺动脉高压的罕见情况，以确定最佳治疗方案。
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