Department of Pediatrics.
Cancer and Blood Disease Institute.
Pediatrics. 2022 May 1;149(5). doi: 10.1542/peds.2021-052974.
An 8-year-old boy with asthma presented with prolonged fever, malaise, extremity weakness, polyarthralgias, malar rash, and subcutaneous nodules. Physical examination was remarkable for a faint malar rash, flesh-colored papules on the dorsal aspect of the fingers, arthritis of multiple joints in the hands, and subcutaneous nodules. The nodules were firm, nontender, and distributed over multiple extremities and the trunk. The patient was admitted to expedite workup. Initial laboratory test results revealed leukopenia, mild elevation of the aminotransferases, an elevated erythrocyte sedimentation rate, and normal level of creatine kinase. His echocardiogram was normal. Infectious disease studies were negative. Additional examination revealed dilated capillaries in his nail beds and bilateral hip weakness. MRI of his extremities was negative for myositis or calcification of the nodules. We obtained a biopsy of the subcutaneous nodules, and because the patient remained afebrile during the hospitalization, we discharged him from the hospital with outpatient follow-up. Our expert panel reviews the course of the patient's evaluation and investigation, as well as the implications of his diagnosis based on the tissue pathology from the nodule biopsy.
一位 8 岁哮喘男孩出现长期发热、乏力、四肢无力、多发性关节炎、面颊皮疹和皮下结节。体格检查可见轻微的面颊皮疹、手指背部的肉色丘疹、双手多个关节的关节炎和皮下结节。结节质地坚硬、无触痛,分布于多个四肢和躯干。患者被收治入院以加快检查。初步实验室检查结果显示白细胞减少、氨基转移酶轻度升高、红细胞沉降率升高和肌酸激酶正常。他的超声心动图正常。传染病研究为阴性。进一步检查发现其甲床毛细血管扩张和双侧髋关节无力。四肢 MRI 检查未见肌炎或结节钙化。我们对皮下结节进行了活检,由于患者在住院期间不再发热,我们让他出院,进行门诊随访。我们的专家小组审查了患者的评估和检查过程,以及根据结节活检的组织病理学对其诊断的影响。